Abstract
The classic clinical presentation of children with Wilms tumor (WT) overlaps with many aspects of the general presentation of abdominal mass in children. However, specific details of the history, physical exam and laboratory evaluation can raise the suspicion of WT even prior to imaging or surgical procedures. Other renal tumors, such as rhabdoid tumor of the kidney (RTK), congenital mesoblastic nephroma (CMN), clear cell sarcoma of the kidney (CCSK), and renal cell carcinoma (RCC), also have particular presenting characteristics that can steer the clinician towards the consideration of those diagnoses.
This chapter will largely address the presentation of children with WT, as the leading renal tumor in children, but will also give brief attention to these less common renal tumors of childhood. We will review both common and uncommon presentations of Wilms tumor through discussion of an evaluation for a child suspected to have either an abdominal mass or a renal tumor. We will review the basic elements of evaluation which should be performed, including history, thorough physical exam, and initial laboratory and radiologic evaluation.
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Mullen, E., Graf, N. (2014). Clinical Presentation. In: Pritchard-Jones, K., Dome, J. (eds) Renal Tumors of Childhood. Pediatric Oncology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-44003-2_3
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DOI: https://doi.org/10.1007/978-3-662-44003-2_3
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