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Pädiatrische Hämatologie und Onkologie pp 551–560Cite as

Seltene Tumoren

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Zusammenfassung

Seltene Tumoren zeichnen sich durch zwei Merkmale aus: ihre Inzidenz ist mit <10 Neudiagnosen/Jahr in Deutschland ausgesprochen niedrig und sie werden nicht in den kooperativen Therapieoptimierungsstudien der GPOH erfasst. Oft wurden Kinder und Jugendliche mit seltenen Tumorerkrankungen daher bislang außerhalb der besonderen Versorgungsstrukturen der Kinderonkologie behandelt. Der Mangel an kompetenten zentralen Ansprechpartnern wurde durch den Terminus »orphan tumors« illustriert. Um Kompetenz, Datenlage und Vernetzung zu verbessern, werden die seltenen Tumorerkrankungen seit 2012 durch das GPOH-Register »Seltene Tumorerkrankungen in der Pädiatrie« (STEP) erfasst. Dieses Register sowie die zunehmende internationale Vernetzung werden es zukünftig ermöglichen, Aussagen zu Häufigkeit und klinischen Besonderheiten bei diesen seltenen Tumorerkrankungen zu treffen und Therapiekonzepte zu entwickeln.

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Authors and Affiliations

  1. Klinik für Kinder- und Jugendmedizin, Klinikum Dortmund, Beurhausstraße 40, 44137, Dortmund, Deutschland

    Prof. Dr. med. D. Schneider

  2. Pädiatrische Onkologie und Hämatologie, Universitätsklinikum Tübingen, Hoppe-Seyler-Str 1, 72076, Tübingen, Deutschland

    Dr. med. I. B. Brecht

  3. Universitätsklinikum Aachen, Zentrum für Kinder-/Jugendmedizin, Pauwelsstr. 30, 52074, Aachen, Deutschland

    Prof. Dr. med. R. Mertens

Authors
  1. Prof. Dr. med. D. Schneider
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  2. Dr. med. I. B. Brecht
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  3. Prof. Dr. med. R. Mertens
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Correspondence to D. Schneider .

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Editors and Affiliations

  1. Universitätsklinik um Freiburg Zentrum für Kinder- und Jugendmedizin, Freiburg, Deutschland

    Charlotte Niemeyer

  2. Charité-Universitätsmedizin Berlin, Berlin, Deutschland

    Angelika Eggert

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Schneider, D., Brecht, I.B., Mertens, R. (2018). Seltene Tumoren. In: Niemeyer, C., Eggert, A. (eds) Pädiatrische Hämatologie und Onkologie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-43686-8_33

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  • DOI: https://doi.org/10.1007/978-3-662-43686-8_33

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