Spongy Degeneration of the Central Nervous System in Infancy

  • Kurt Jellinger
  • Franz Seitelberger
Conference paper
Part of the Current Topics in Pathology book series (CT PATHOLOGY, volume 53)


Progressive degenerative subcortical encephalopathy; Early infantile familial cerebral sclerosis; Early infantile “diffuse sclerosis” of the brain; Idiotie familiale avec dégénérescence spongieuse du névraxe; Familial idiocy with spongy degeneration of the neuraxis; Spongy degeneration of the cerebral white matter; Spongy type of diffuse sclerosis; Familial idiocy with spongy degeneration of the CNS; Spongy degeneration of the CNS in infancy; Spongy degeneration of the nervous system; dégénérescence spongieuse familiale; Ödemkrankheit des ZNS im frühen Kindesalter; Maladie oedémateuse progressive cérébrale de la première enfance; Idiotie amaurotique atypique; Canavan’s sclerosis (disease); Familial spongy degeneration of the brain; Canavan’s spongy degeneration; Diffuse Form der spongiösen Dystrophien des Nervensystems — Typ Canavan; Spongy degeneration of the CNS (van Bogaert-Bertrand type).


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Copyright information

© Springer-Verlag Berlin Heidelberg 1970

Authors and Affiliations

  • Kurt Jellinger
    • 1
  • Franz Seitelberger
    • 1
  1. 1.Neurological Institute of University of ViennaAustria

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