Clinical Presentation and Treatment

  • Max J. Coppes
  • Christine Campbell
  • Bryan R. G. Williams
Part of the Molecular Biology Intelligence Unit book series (MBIU)


In the past two decades, there has been a considerable improvement in the understanding and management of Wilms tumor and other primary renal childhood malignancies. Wilms tumor is usually diagnosed in children under the age of six, although occasionally older children are affected. Current treatment for Wilms tumor includes surgery and chemotherapy for all patients and radiation therapy for those with advanced disease or specific adverse prognostic features. This has led to cure rates exceeding 80%,1 permitting most affected children to reach adulthood.


Genitourinary Malformation Drash Syndrome Natl Cancer Lnst WAGR Syndrome Mulibrey Nanism 
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Copyright information

© Springer-Verlag Berlin Heidelberg 1995

Authors and Affiliations

  • Max J. Coppes
    • 1
  • Christine Campbell
    • 2
  • Bryan R. G. Williams
    • 2
  1. 1.Tom Baker Cancer Centre and University of CalgaryCalgaryCanada
  2. 2.Department of Cancer Biology Research InstituteCleveland Clinic FoundationClevelandUSA

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