Zusammenfassung
Bei den primären Immundefekten handelt es sich vorwiegend um sehr seltene Erkrankungen, deren Inzidenz vielfach in der Größenordnung von 1:1.000.000 oder darunter liegt. Das Management dieser Patienten erfordert daher die enge Zusammenarbeit zwischen dem betreuenden Haus- oder Kinderarzt, Ärzten aus immunologischen Schwerpunktzentren sowie weiteren Fachärzten wie z. B. Dermatologen, Pulmonologen und Gastroenterologen. Die Therapieeinleitung wird in immunologischen Schwerpunktzentren begonnen, in denen die Patienten auch in regelmäßigen Abständen vorstellig werden sollten.
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Schröder, J.O. et al. (2003). Immunologisch bedingte Krankheiten. In: Schölmerich, J., et al. Medizinische Therapie in Klinik und Praxis. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-12451-2_3
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