Restriktive Kardiomyopathie

  • M. Böhm


Die restriktive Kardiomyopathie ist eher selten und zeichnet sich durch eine zunehmende Steifigkeit des Herzens mit Beteiligung des Myokards, des Intertitiums und des Endokards aus (Kushawa et al. 1997). Die Steifigkeit kann durch eine vermehrte endomyokardiale Fibrosierung, aber auch durch Einlagerung von Proteinen (z. B. Amyloid) bedingt sein. Das Ausmaß der hämodynamischen Beeinträchtigung korreliert nicht zwingend mit den histopathologisch beobachteten Veränderungen (Keren u. Popp 1992).


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© Springer-Verlag Berlin Heidelberg 2000

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  • M. Böhm

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