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Systemkrankheiten mit Beteiligung des Respirationstraktes

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Zusammenfassung

Rheumatische Erkrankungen können verschiedene anatomische Strukturen der Atemwege und der Lunge betreffen. Am bekanntesten ist die Pleuritis bei Morbus Still, der systemischen Form der juvenilen idiopathischen Arthritis. Rheumatische Krankheiten können aber auch das Lungengewebe als interstitielle Pneumonitis mit der möglichen Folge einer Lungenfibrose betreffen. Obstruktive Ventilationsstörungen finden sich als Folge einer subglottischen Stenose oder Bronchusstenose bei der Wegener-Granulomatose. Bei der Dermatomyositis kann es durch die Schwäche der Atemmuskulatur bis zur respiratorischen Insuffizienz kommen. Eine mangelnde Dehnbarkeit der Thoraxwand kann bei der Sklerodermie zu einer restriktiven Ventilationsstörung führen.

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© 2004 Springer-Verlag Berlin Heidelberg

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Weißbarth-Riedel, E., Rieger, C., Paul, K., Teig, N., von der Hardt, H., Stephan, V. (2004). Systemkrankheiten mit Beteiligung des Respirationstraktes. In: Rieger, C., von der Hardt, H., Sennhauser, F.H., Wahn, U., Zach, M. (eds) Pädiatrische Pneumologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-09182-1_13

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  • DOI: https://doi.org/10.1007/978-3-662-09182-1_13

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-09183-8

  • Online ISBN: 978-3-662-09182-1

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