Die Anomalien des Einflußtraktes des rechten Ventrikels

  • F. Helmer
Part of the Allgemeine und spezielle Operationslehre book series (OPERATIONSLEHRE, volume 6 / 2)


Die wichtigsten Anomalien des Einflußtraktes des rechten Ventrikels sind die Hypoplasie, die Trikuspidalatresie und Stenose, der Morbus Ebstein und die Uhlsche Erkrankung. Der hypoplastische rechte Ventrikel (hypoplastisches Rechtsherz) kommt isoliert (Gasul et al., 1959; Hauwaert u. Hichaelsson, 1971) oder kombiniert mit Pulmonal- oder Trikuspidalatresie bzw. Stenose und Vorhofseptumdefekt vor (Potts et al., 1946; Phoury et al., 1969; Riker et al., 1963). Alle diese Anomalien sind selten, so wurde die kombinierte Form der Hypoplasie in etwa 5%, die Trikuspidalatresie in 2 – 5%, der Morbus Ebstein in knapp 1% und die Uhlsche Erkrankung unter 0, 1% bei 1000 autopsierten angeborenen Herzfehlern beobachtet (Bankl, 1975).


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  1. Azzolina, G., Eufrate, S., Pensa, P.: Tricuspid atresia: Experience in Surgical management with a modified cava-pulmonary anastomosis. Thorax 27, 111 – 115 (1972).PubMedCrossRefGoogle Scholar
  2. Bahnson, H., Bauersfeld, S.R., Smith, J.W.: Pathological Anatomy and Surgical Correction of Ebstein’s anomaly. Circulation 31 und 32, Suppl. I, 1–8 (1965).CrossRefGoogle Scholar
  3. Bakulev, A.N., Kolesnikov, S.A.: Anastomosis of superior vena cava and pulmonary artery in the surgical treatment of certain congenital defects of the heart. J. thorac. Surg. 37, 693 (1959)PubMedGoogle Scholar
  4. Bankl, H.: Congenital Malformations of the Heart and Great Vessels. München-Baltimore: Urban & Schwarzenberg 1977.Google Scholar
  5. Barbero-Marcial, N., Nuno-Conceicao, A., Verginelli, G., Ebaid, M., Snitcowsky, R., Zerbini, E.J.: Congenital tricuspid stenosis treated by a palliative open operation. J. thorac. cardiovasc. Surg. 69, 562–567(1975).PubMedGoogle Scholar
  6. Barnard, C.N., Schrire, V.: Surgical correction of Ebstein’s malformation with prosthetic tricuspid valve. Surgery 54, 302–308 (1963).PubMedGoogle Scholar
  7. Blalock, A., Taussig, H.B.: The surgical treatment of malformations of the heart in which there is pulmonary stenosis or pulmonary atresia. J. Amer. med. Ass. 128, 189 (1945).CrossRefGoogle Scholar
  8. Cartwright, R.S., Smeloff, E.A., Cayler, G.G., Fong, W.Y., Huntley, A.C., Blake, J.R., McFall, R.A.: Total Correction of Ebstein’s Anomaly by Means of Tricuspid Replacement. J. thorac. cardiovasc. Surg. 47, 755–761 (1964).PubMedGoogle Scholar
  9. Deverall, P.B., Lincoln, J.C.R., Aberdeen, E., Bonham-Carter, R.E., Waterston, D.J.: Surgical management of tricuspid atresia. Thorax 24, 239–245 (1969).PubMedCrossRefGoogle Scholar
  10. Ebstein, W.: Über einen sehr seltenen Fall von Insuffizienz, bedingt durch eine hochgradige Mißbildung derselben. Arch. anat. physiol. Wissensch. 1866, 238–254.Google Scholar
  11. Edwards, J.E., Burchell, H.B.: Congenital Tricuspid Atresia: A Classification. Med. Chir. N. Amer. 33, 1117–1196(1949).Google Scholar
  12. Edwards, W.S., Bargeron, L.M.: The superiority of the Glenn operation for tricuspid atresia in infancy and childhood. J. thorac. cardiovasc. Surg. 55, 60–69 (1968).PubMedGoogle Scholar
  13. Fontan, F., Baudet, E.: Surgical repair of tricuspid atresia. Thorax 26, 240 (1971).PubMedCrossRefGoogle Scholar
  14. Fontan, F., Choussat, A.: Trata miento quirúrgico de la atresia tricuspidea. Hosp. Gen. XV, 407–416(1975).Google Scholar
  15. Gams, E., Meisner, H., Peak, S.U., Sebening, F.: Korrektur-Operation bei Morbus Ebstein. Thoraxchirurgie u. Vask. Chir. in Druck (1977).Google Scholar
  16. Gasul, B.M., Weinberg, M., Luan, L.L., Fell, E.H., Bicoff, J.: Superior vena cava-right main pulmonary artery anastomosis: Surgical correction for patients with Ebstein’s anomaly and for congenital hypoplastic right ventricle. J. Amer. med. Ass. 171, 1797 (1959).CrossRefGoogle Scholar
  17. Glenn, W.W.L., Patino, J.F.: Circulatory bypass of the right heart. I. Preliminary observations on the direct delivery of vena caval blood into the pulmonary artery circulation. Azygos vein pulmonary artery shunt. Yale J. Biol. Med. 27, 147 (1954).PubMedGoogle Scholar
  18. Glenn, W.W.L., Gardner, T.H., Talner, N.S., Stansel, H.C., Matano, I.: Rational Approach to the Surgical Management of Tricuspid Atresia. Circulation 37 and 38, II62–II67 (1967).Google Scholar
  19. Hardy, K.L., May, I.A., Webster, C.A., Kimball, K.G.: Ebstein’s anomaly: A functional Definitive Repair. J. thorac. cardiovasc. Surg. 48, 927–940 (1964).PubMedGoogle Scholar
  20. Hardy, K.L., Roe, B.: Ebstein’s anomaly. Further experience with definitive repair. J. thorac. cardiovasc. Surg. 58, 553–561 (1969).PubMedGoogle Scholar
  21. Hauwaert van der, L.G., Miachaelsson, M.: Isolated right ventricular hypoplasia. Circulation 44, 466–474(1971).PubMedCrossRefGoogle Scholar
  22. Henry, J.N., Devloo, R.A.E., Ritter, D.G., Mair, D.D., Davis, G.D., Danielson, G.K.: Tricuspid Atresia. Successful Surgical “Correction” in Two Patients Using Porcine Xenograft Valves. Proc. Mayo Clin. 49, 803–810 (1974).PubMedGoogle Scholar
  23. Hunt, D., Edwards, W.S., Deverall, P.B., Bargeron, L.M., Jr.: Superior vena cava to right pulmonary artery anastomosis. Thorax 25, 550 – 555 (1970).PubMedCrossRefGoogle Scholar
  24. Hunter, S.W., Lillehei, C.W.: Ebstein’s Malformation of the Tricuspidal Valve. Dis. Chest. 33, 297–304(1958).PubMedCrossRefGoogle Scholar
  25. Kay, J.H., Tsuji, H.K., Redington, J.V., Yamada, T., Kagawa, A., Shima, Y.: The Surgical Treatment of Ebstein’s Malformation with right Ventricular Aneurysmorrhaphy and Replacement of the Tricuspidal Valve with a Disc Valve. Dis. Chest. 51, 537–540 (1967).PubMedCrossRefGoogle Scholar
  26. Keith, J.D., Rowe, R.D., Vlad, P.: Heart Disease in Infancy and Childhood. New York: Macmillan 1958.Google Scholar
  27. Khoury, G.H., Gilbert, E.F., Chang, C.H., Schmidt: The Hypoplastic Right Heart Complex. Amer. J. Cardiol. 23, 792 (1969).PubMedCrossRefGoogle Scholar
  28. Koncz, J.: Die Cavo-pulmonale Anastomose. Thoraxchirurgie und vaskul. Chirurgie 11, 105 – 115 (1963–1964).Google Scholar
  29. Kreutzer, G., Galindez, E., Bono, H., Palma de, D., Laura, J.P.: An operation for the correction of tricuspid atresia. J. thorac. cardiovasc. Surg. 66, 613 – 621 (1973).PubMedGoogle Scholar
  30. Lillehei, C.W., Kalke, B.R., Carlson, R.G.: Evolution of Corrective Surgery for Ebstein’s Anomaly. Circulation 36, Suppl. I, 111 – 118 (1967).Google Scholar
  31. Mannix, E.P., Jr., Berroya, R.B.: Prosthetic replacement of the tricuspid valve of Ebstein’s anomaly. J. cardiovasc. Surg. 12, 355–365 (1971).Google Scholar
  32. Mathur, M., Glenn, W.W.L.: Long-term evaluation of cava-pulmonary artery anastomosis. Surgery 74, 899–916 (1973).PubMedGoogle Scholar
  33. McFaul, R.C., Davis, Z., Giuliani, E.R., Ritter, D.G. u. Danielson, G.K.: Ebstein’s malformation: Surgical experience at the Mayo Clinic, J. thorac. cardiovasc. Surg. 72, 910–915, 1976.PubMedGoogle Scholar
  34. Meisner, H., Klinner, W., Schmidt-Habelmann, P., Sebening, F.: Zur Chirurgie des Morbus Ebstein. Langenbecks Arch. Chir. 320, 307–321 (1968).PubMedCrossRefGoogle Scholar
  35. Ostermeyer, J.: Uhl’s Disease: Partial Parchment Right Ventricle. Virchows Arch. path. Anat. and Histol. 362, 185–194 (1974).CrossRefGoogle Scholar
  36. Potts, W.J., Smith, S., Gibson, S.: Anastomosis of the Aorta to a pulmonary artery; certain types in congenital heart disease. J. Amer. med. Ass. 132, 627 (1946).CrossRefGoogle Scholar
  37. Riker, L.W., Potts, W.J., Grana, L., Miller, R.A., Lev, M.: Tricuspid stenosis or atresia complexes. A Surgical and Pathologic Analysis. J. thorac. cardiovasc. Surg. 45, 423–433 (1963).PubMedGoogle Scholar
  38. Rittenhouse, E.A., Mohri, H., Yates, W.G., Tenckhoff, L., Reichenbach, D.D., Merendino, K.A.: Ventricular enlargement for underdeveloped right ventricle and associated anomalies. J. thorac. cardiovasc. Surg. 68, 229–236 (1974).PubMedGoogle Scholar
  39. Robicsek, A., Temesvar, A., Kadar, P.L.: A new Method for the Treatment of Congenital Heart Disease. Associated with impaired Pulmonary Circulation. Acta med. scand. 154, 151 (1956).PubMedCrossRefGoogle Scholar
  40. Scott, L.P., III, Dempsey, J.J., Timmis, H.H., Clenathan, J.E.: A Surgical Approach to Ebstein’s Disease. Circulation 27, 574–577 (1963).PubMedCrossRefGoogle Scholar
  41. Senoo, Y., Ohishi, K., Nawa, S., Teramoto, S., Sunada, T.: Total correction of Ebstein’s anomaly by replacement with a biological aortic valve without plication of the atrialized ventricle. J. thorac. cardiovasc. Surg. 72, 243–248 (1976).PubMedGoogle Scholar
  42. Shumacker, H.B., Jr.: Miscellaneous congenital cardiac anomalies. In: Gibbon, J.H., Jr., Sabiston, D.C., Jr., Spencer, F.C.: Surgery of the Chest, 2nd Ed. Philadelphia-London-Toronto: Saunders 1969.Google Scholar
  43. Tandon, R., Edwards, J.E.: Tricuspid Atresia A-re-evaluation and Classification. J. thorac. cardiovasc. Surg. 67, 530–542 (1974).PubMedGoogle Scholar
  44. Timmis, H.H., Hardy, J.D., Watson, D.G.: The Surgical Management of Ebstein’s Anomaly. The combined use of tricuspid atrioventricular plication and atrioplasty. J. thorac. cardiovasc. Surg. 53, 385–391 (1967).PubMedGoogle Scholar
  45. Uhl, H.S.M.: A previously undescribed congenital malformation of the heart: almost total absence of the myocardium of the right ventricle. Bull. Johns Hopk. Hosp. 91, 197 (1952).Google Scholar
  46. Waterston, D.J.: Treatment of Fallot’s tetralogy in children under 1 year of age. Rohzl. Chir. 41, 181 (1962).Google Scholar
  47. Young, W.G., Jr., Flemma, R.J.: The Present Status of the Caval-Pulmonary Anastomosis. Dis. Chest 50, 87–92(1966).PubMedCrossRefGoogle Scholar

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© Springer-Verlag Berlin Heidelberg 1978

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  • F. Helmer

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