Pathophysiologically, defect dysproteinemias represent the situations where certain plasma protein components show isolated deficiency. Therefore, they include mostly the congenital forms of plasma protein deficiencies. For the purposes of clinical differentiation, some acquired or secondary protein deficiency states will be briefly discussed. Congenital protein deficiency is a condition where the protein synthesis within the cells is deficient, due to various reasons that are discussed elsewhere (page 105). Some of the important plasma protein deficiencies are listed in Fig. 241. Among these plasma protein deficiencies, the one which causes a significant hypoproteinemia is congenital analbuminemia. Complete deficiency of other plasma protein components may not necessarily accompany hypoproteinemia.
KeywordsPrimary Immunodeficiency Serum Immunoglobulin Level Hematological Finding Chronic Lymphatic Leukemia Immunological Finding
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