Mastocytosis covers a wide spectrum of a proliferative diseases of mast cells in the skin and/or in internal organs. We recognize different subtypes of mastocytosis: (a) mastocytoma, (b) urticaria pigmentosa, (c) diffuse cutaneous mastocytosis, (d) telangiectasia macularis eruptiva perstans (TMEP), (e) systemic mastocytosis and (f) mast cell leukemia. The most common manifestation of mastocytosis is urticaria pigmentosa, which is characterized by small or larger brown-red maculopapules on the skin. Skin is the organ mostly or only involved, but occasionally other organs are also infiltrated. In particular, as a second organ, the bones maybe involved.
KeywordsMast Cell Bullous Pemphigoid Epidermolysis Bullosa Systemic Mastocytosis Disodium Cromoglycate
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