Adamantiades-Behçet’s Disease

  • C. C. Zouboulis

Abstract

Adamantiades-Behçet’s disease is a relapsing-remitting multisystemic inflammatory disorder of unknown etiology, classified as systemic vasculitis and characterised by oral and genital ulcers, cutaneous lesions and uveitis. It is distributed world-wide. However, it occurs endemically in the Eastern Mediterranean and in Middle and Far Eastern countries and is rare among inhabitants of Northern European countries, in Central and Southern Africa, in the Americas and in Australia. The highest prevalence has been reported in Turkey (Anatolia, 370:100 000), in Iran (100:100 000) and in Japan (13.5:100 000).

Synonyms

Behçet’s disease Behçet’s syndrome 

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© Springer-Verlag Berlin Heidelberg 2000

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  • C. C. Zouboulis

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