Abstract
Creutzfeldt-Jakob disease (CJD) is also called subacute spongiform encephalopathy. CJD is a rare transmissible disorder of the CNS which usually becomes manifest in middle-age or the presenile period and ends in death, in many cases within 3–12 months of onset. The disease affects both sexes equally and may be familial. It has been recorded in most parts of the world.
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Bockman JM, Kingsbury DT, McKinley MP, Bendheim PE, et al. (1985) Creutzfeldt-Jakob disease prion proteins in human brains. N Engl J Med 312: 73–78
Bots GTHAM, Man de JCH, Verjaal A (1971) Virus-like particles in brain tissue from two patients with CreutzfeldtJakob disease. Acta Neuropathol 18: 267–270
Brown P, Coker-Vann M, Pomeroy K, Franko M, et al. (1986) Diagnosis of Creutzfeldt-Jakob disease by western blot identification of marker protein in human brain tissue. N Engl J Med 314: 547–551
Chou SM, Martin JD (1971) Kuru-plaques in a case of Creutzfeldt-Jakob disease. Acta Neuropathol 17: 150–155
Cruz-Sanchez F, Lafuente J, Gertz HJ, Stoltenburg-Didinger G (1987) Spongiform encephalopathy with extensive involvement of white matter. J Neurol Sci 82: 81–87
Diringer H, Gelderblom H, Hilmert H, Ozel M, et al. (1983) Scrapie infectivity, fibrils and low molecular weight protein. Nature 306: 476–478
Field EJ, Narang HK (1972) An electron-microscopic study of scrapie in the rat: Further observations on “Inclusion Bodies” and virus-like particles. J Neurol Sci 17: 347–364
Fields BN (1987) Powerful prions? N Engl J Med 317: 1597–1598
Harrington MG, Merril CR, Asher DM, Gajdusek DC (1986) Abnormal proteins in the cerebrospinal fluid of patients with Creutzfeldt-Jakob disease. N Engl J Med 315: 279–282
Macchi G, Abbamöndi AL, Di Trapani G, Sbriccoli A (1984) On the white matter lesions of the Creutzfeldt-Jakob disease. J Neurol Sci 63: 197–206
Manuelidis L (1985) Creutzfeldt-Jakob disease prion proteins in human brains. N Engl J Med 312: 1643–1644
Masters CL, Harris JO, Gajdusek DC, Gibbs CJ, et al. (1979) Creutzfeldt-Jakob disease: Patterns of worldwide occurrence and the significance of familial and sporadic clustering. Ann Neurol 5: 177–188
Merz PA, Somerville RA, Wisniewski HM, Iqbal K (1981) Abnormal fibrils from scrapie-infected brain. Acta Neuropathol 54: 63–74
Merz PA, Somerville RA, Wisniewski HM, Manuelidis L, et al. (1983) Scrapie-associated fibrils in Creutzfeldt-Jakob disease. Nature 306: 474–476
Mizutani T, Okumura A, Oda M, Shiraki H (1981) Panencephalopathic type of Creutzfeldt-Jakob disease: Primary involvement of the cerebral white matter. J Neurol Neurosurg Psychiatry 44: 103–115
Monreal J, Collins GH, Masters CL, Fisher CM, et al. (1981) Creutzfeldt-Jakob disease in an adolescent. J Neurol Sci 52: 341–350
Park TS, Kleinman GM, Richardson EP (1980) CreutzfeldtJakob disease with extensive degeneration of white matter. Acta Neuropathol 52: 239–242
Prusiner SB (1987) Prions and neurodegenerative diseases. N Engl J Med 317: 1571–1581
Ridley RM, Baker HF, Crow TJ (1985) Virogenes in scrapie and Creutzfeldt-Jakob disease. J R Soc Med 78: 970
Roberts GW, Brown R, Crow TJ, Barry RA, et al. (1986) Prion-protein immunoreactivity in human transmissible dementias. N Engl J Med 315: 1231–1232
Roos R, Gajdusek DC, Gibbs CJ (1973) The clinical characteristics of transmissible Creutzfeldt-Jakob disease. Brain 96: 1–20
Rossum van A (1968) Spastic pseudosclerosis. In: Vinken PJ, Bruyn GW, eds. Handbook of clinical neurology, vol 6. Amsterdam: North Holland Publishing Company: 726–760
Tateishi J, Nagara H, Hikita K, Sato Y (1984) Amyloid plaques in the brains of mice with Creutzfeldt-Jakob disease. Ann Neurol 15: 278–280
Tateishi J, Ohta M, Kuroiwa Y (1978) Subacute spongiform encephalopathy with Kuru plaques and its successful transmission to the small rodents. J Neuropathol Exp Neurol 37: 699
Tateishi J, Ohta M, Koga M, Sato Y, et al. (1979) Transmission of chronic spongiform encephalopathy with kuru plaques from humans to small rodents. Ann Neurol 5: 581–584
Tomlinson BE, Corsellis JAN (1984) Ageing and the dementias. In: Hume Adams J, Corsellis JAN, Duchen LW, eds. Greenfield’s Neuropathology, 4th ed. London: Edward Arnold: 951–1025
Vernon ML, Horta-Barbosa L, Fuccillo DA, Sever JL, et al. (1970) Virus-like particles and nucleo-protein-type filaments in brain tissue from two patients with CreutzfeldtJakob disease. Lancet I: 964–966
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© 1989 Springer-Verlag Berlin Heidelberg
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Valk, J., van der Knaap, M.S. (1989). Creutzfeldt-Jakob Disease. In: Magnetic Resonance of Myelin, Myelination, and Myelin Disorders. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-02568-0_38
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DOI: https://doi.org/10.1007/978-3-662-02568-0_38
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