Dermatology pp 1289-1292 | Cite as

The Hyalinoses

  • Otto Braun-Falco
  • Gerd Plewig
  • Helmut H. Wolff
  • Walter H. C. Burgdorf


Hyalin is a poorly understood and even poorly defined word. It means “glassy or translucent substance” and has been applied to proteins that are amorphous and stain in such a fashion but lack other distinguishing characteristics. Hyaline is the corresponding adjective. In the skin, a hodgepodge of different materials have been identified. Some authors include amyloid and gouty tophi under hyalins; others specifically exclude these substances. The overproduction of carbohydrate-rich glycoproteins is the usual explanation for their genesis. Several exceedingly rare disorders are traditionally considered “hyalinoses”.


Human Skin Fibroblast Proteus Syndrome Autosomal Recessive Pattern Gouty Tophus Hyaline Material 
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Copyright information

© Springer-Verlag Berlin Heidelberg 2000

Authors and Affiliations

  • Otto Braun-Falco
    • 1
  • Gerd Plewig
    • 1
  • Helmut H. Wolff
    • 2
  • Walter H. C. Burgdorf
    • 1
  1. 1.Department of Dermatology and AllergologyLudwig Maximilians UniversityMunichGermany
  2. 2.Department of Dermatology and VenerologyUniversity of LübeckLübeckGermany

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