Dermatology pp 697-708 | Cite as

Pustular Diseases

  • Otto Braun-Falco
  • Gerd Plewig
  • Helmut H. Wolff
  • Walter H. C. Burgdorf


One unusual feature of the skin is its tendency to form sterile pustules. Nondermatologists have often been taught to equate pus with infection and find the nonchalance of dermatologists’ approach to pus puzzling. While many bacterial, viral, and fungal infections in the skin are indeed pustular, there are also many patients who present with sterile pustules. The prototypical pustular disease is psoriasis. Presumably, a number of noninfectious triggers can also produce the appropriate cytokines for eliciting a pustular response in the skin. In this chapter, we will discuss the idiopathic pustular diseases, dividing them as shown in Table 16.1 into acral and generalized conditions while also distinguishing between the childhood and adult forms.

Table 16.1

Idiopathic pustular diseases

Localizd acral pustules


Infantile acropustulosis


Parakeratosis pustulosa


Acrodermatitis continua suppurativa


Palmoplantar pustulosis


Acute acropustulosis


Erosive pustular dermatosis


of the scalp

Generalized pustules


Erythema toxicum neonatorum


Transient neonatal pustular melanosis


Incontinentia pigmenti


IgA pemphigus foliaceus


Subcorneal pustular dermatosis


Impetigo herpetiformis


Acute generalized exanthematous




Eosinophilic pustular folliculitis


Pustular Psoriasis Acute Generalize Exanthematous Pustulosis SAPHO Syndrome Generalize Pustular Psoriasis Palmoplantar Pustulosis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Erythema Toxicum Neonatorum

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Impetigo Herpetiformis

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Copyright information

© Springer-Verlag Berlin Heidelberg 2000

Authors and Affiliations

  • Otto Braun-Falco
    • 1
  • Gerd Plewig
    • 1
  • Helmut H. Wolff
    • 2
  • Walter H. C. Burgdorf
    • 1
  1. 1.Department of Dermatology and AllergologyLudwig Maximilians UniversityMunichGermany
  2. 2.Department of Dermatology and VenerologyUniversity of LübeckLübeckGermany

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