Advertisement

Desmoid-Aggressive Fibromatosis

Chapter
  • 86 Downloads
Part of the Medical Radiology book series (MEDRAD)

Abstract

Following surgical excision alone, local recurrences occur in 27–57 percent of cases of desmoid — aggressive fibromatosis. Radiation therapy in doses of 5000–6000 rad decreases local recurrence rates. Normal tissue tolerance may be limiting for the total dose of external beam radiation; therefore either post-operative brachytherapy or brachytherapy following external beam may be used. Regression rates may occur from eight months to two years following treatment. Desmoid — aggressive fibromatosis may occur in association with Gardner’s syndrome and pregnancy. A seventy percent local control rate has been reported with external radiation. In the national survey eighty-two percent of radiation oncologists would treat desmoid — aggressive fibromatosis.

Keywords

Desmoid Tumor Cystic Hygroma Aggressive Fibromatosis Normal Tissue Tolerance Roentgen Therapy 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

References

  1. 1.
    Assad WA, Nori D, Hilaris BS, Shiu MH and Hajdu SI (1986) Role or brachytherapy in the management of desmoid tumors. Int J Radiation Oncology Biol Phys 12 :901–906.CrossRefGoogle Scholar
  2. 2.
    Khorsand J and Karakousis CP (1985) Desmoid tumors and their management. Am J Surg 149 :215–218.PubMedCrossRefGoogle Scholar
  3. 3.
    Reitamo JJ (1983) The desmoid tumor IV. Choice of treat-ment results and complications. Arch Surg 118 :1318–1322.PubMedCrossRefGoogle Scholar
  4. 4.
    Leibel SA, Wara WM, Hill DR, Bovill EG, DeLorimer AA, Beckstead JH and Phillips TL (1982) Desmoid tumors: Local control and patterns of relapse following radiation therapy. Int J Radiation Oncol Biol Phys 9 :1167–1171.Google Scholar
  5. 5.
    Greenberger HM, Goebel R, Weichselbaum RR, Greenberger JS, Chaffey JT and Cassady JR (1981) Radiation therapy in treatment of aggressive fibromatosis. Int J Radiation Oncol Biol Phys 7: 305–310.CrossRefGoogle Scholar
  6. 6.
    Abadir R (1976) Desmoid tumor associated with cystosar-coma phylloides of the breast. J Surg Onco1 8: 43–48.CrossRefGoogle Scholar
  7. 7.
    Suit HD and Russell WO (1975) Radiation therapy of soft tissue sarcomas. Cancer 36 :759–764.PubMedCrossRefGoogle Scholar
  8. 8.
    Hill DR, Newman H and Phillips TL (1973) Radiation therapy of desmoid tumors. Am J Roent Rad Ther Nucl 17 :84–89.Google Scholar
  9. 9.
    Gaches C and Burke J (1971) Desmoid tumor (fibroma of the abdominal wall) occurring in siblings. Br J Surg 58 :495–498.PubMedCrossRefGoogle Scholar
  10. 10.
    Brasfield RD and Das Gupta TK (1969) Desmoid tumors 19. of the anterior abdominal wall. Surgery 65 :241–246.PubMedGoogle Scholar
  11. 11.
    Cole NM and Guiss LW (1969) Extra-abdominal desmoid tumors. Arch Surg 98 :530–533.PubMedCrossRefGoogle Scholar
  12. 12.
    Enzinger FM and Shiraki M (1967) Musculo-aponeurotic fibromatosis of the shoulder girdle (extra-abdominal desmoid). Cancer 20 :1131–1140.PubMedCrossRefGoogle Scholar
  13. 13.
    Masson JK and Soule EH (1966) Desmoid tumors of the head and neck. Am J Surg 112 :615–622.PubMedCrossRefGoogle Scholar
  14. 14.
    Rosen RS and Kimball W (1966) Extra-abdominal desmoid tumor. Radiology 86 :534–540.PubMedGoogle Scholar
  15. 15.
    Benninghoff D and Robbins R (1964) The nature and treatment of desmoid tumors. Am J Roent Rad Ther Nucl Med 91 :132–137.Google Scholar
  16. 16.
    Dahn I, Jonsson N and Lundh G (1963) Desmoid tumors. Acta Chir Scand 126 :305–314.PubMedGoogle Scholar
  17. 17.
    Soule EH and Scanlon PW (1962) Fibrosarcoma arising in an extra-abdominal desmoid tumor: Report of a case. Staff Meetings of the Mayo Clinic 37 :443–451.Google Scholar
  18. 18.
    Gonatas NK (1961) Extra-abdominal desmoid tumors. Arch Path 71 :214–221.PubMedGoogle Scholar
  19. 19.
    Hunt RT, Morgan HC and Ackerman LV (1960) Principles in the management of extra-abdominal tumors. Cancer 13 :825–836.PubMedCrossRefGoogle Scholar
  20. 20.
    Musgrove JE and McDonald JR (1948) Extra-abdominal desmoid tumors. Arch Path 45 :513–540.PubMedGoogle Scholar
  21. 21.
    Pack GT and Ehrlich HE (1944) Neoplasms of the anterior abdominal wall with special consideration of desmoid tumors. Int Abst Surg 79 :177–198.Google Scholar
  22. 1.
    Ketchum LD and Hixson FP (1987) Dermofasciectomy and full-thickness grafts in the treatment of Dupuytren’s contracture. J Hand Surg Am 12 :659–664.PubMedGoogle Scholar
  23. 2.
    Schneider LD, Hankin FM and Eisenberg T (1986) Surgery of Dupuytren’s disease: A review of the open palm method. J Hand Surg Am 11 :23–27.PubMedGoogle Scholar
  24. 3.
    Matton G and Beck F (1982) Our experience with 186 operated Dupuytren hands. Comparison of two techniques. Acta Orthop Belg 48 :775–793.PubMedGoogle Scholar
  25. 4.
    Robbins TH (1981) Dupuytren’s contracture: The deferred z-plasty. Ann R Coll Surg Engl 63 :357–358.PubMedGoogle Scholar
  26. 5.
    Tubiana R, Fahrer M and McCullough CJ (1981) Recurrence and other complications in surgery of Dupuytren’s contracture. Clin Plast Surg 8 :45–50.PubMedGoogle Scholar
  27. 6.
    Orlando JC, Smith JW and Goulian D (1974) Dupuytren’s contracture: A review of 100 patients. Br J Plast Surg 27 :211–217.PubMedGoogle Scholar
  28. 7.
    Viganto JA (1973) Dupuytren’s contracture: A review. Semin Arthritis-Rheum 3 :155–176.CrossRefGoogle Scholar
  29. 8.
    Quetglas J (1972) Dupuytren’s disease. Comments on 80 cases operated on. Acta Chir Plast 14 :244–254.PubMedGoogle Scholar
  30. 9.
    Honner R, Lamb DW and James JIP (1971) Dupuytren’s contracture. Long term results after fasciectomy. J Bone & Joint Surg Am 53 :240–246.Google Scholar
  31. 10.
    McFarlane RM and Jamieson WG (1966) Dupuytren’s contracture. The management of one hundred patients. J Bone & Joint Surg Am 48 :1095–1125.Google Scholar
  32. 11.
    Webb-Jones A (1965) Dupuytren’s contracture. The results of radical fasciectomy. Br J Plast Surg 18 :377–384.PubMedCrossRefGoogle Scholar
  33. 12.
    Finney R (1955) Dupuytren’s contracture. Br J Rad 28 :610–614.CrossRefGoogle Scholar
  34. 13.
    Finney R (1953) Dupuytren’s contracture. Lancet 2 :1064–1066.CrossRefGoogle Scholar
  35. 14.
    Skoog TS (1948) Dupuytren’s contracture with special reference to etiology and improved surgical treatment; its occurence in epileptics; note on knuckle-pads. Acta Scand 96 :1–190.Google Scholar
  36. 15.
    Beatty SR (1938) Roentgen therapy of Dupuytren’s contracture. Rad 30 :610–612.Google Scholar

Copyright information

© Springer-Verlag Berlin Heidelberg 1990

Authors and Affiliations

  1. 1.The Johns Hopkins HospitalBaltimoreUSA
  2. 2.School of MedicineStanford UniversityStanfordUSA

Personalised recommendations