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Zusammenfassung

Die primär biliäre Zirrhose entwickelt sich aus einer Entzündung an intrahepatischen Gallenwegen. Diese chronische, nicht eitrige, destruierende Cholangitis ist nur langsam progredient. Die Entzündung greift von den Portalfeldern auf das Leberparenchym über und endet schließlich in einer Zirrhose. 90% der Patienten sind Frauen. Die mittlere Lebenserwartung von Patienten mit Symptomen liegt bei ungefähr 10 Jahren [1]. Patienten ohne Symptome haben eine günstige Prognose und entwickeln über Jahre hinweg oft weder Symptome, noch eine Leberzirrhose [2]. Sie bedürfen keiner Therapie.

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© 1982 Springer-Verlag Berlin Heidelberg

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Fölsch, U.R., Junge, U. (1982). Besondere Zirrhoseformen. In: Medikamentöse Therapie in der Gastroenterologie. Kliniktaschenbücher. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-96689-7_19

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  • DOI: https://doi.org/10.1007/978-3-642-96689-7_19

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-11389-8

  • Online ISBN: 978-3-642-96689-7

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