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Das kongenitale nephrotische Syndrom

Conference paper
Part of the Ergebnisse der Inneren Medizin und Kinderheilkunde book series (KINDERHEILK. NF, volume 30)

Zusammenfassung

Im Laufe des letzten Vierteljahrhunderts hat man von der klinisch klar umrissenen, aber hinsichtlich ihrer Ätiologie noch immer rätselhaften Krankheitseinheit des nephrotischen Syndroms eine bei Neugeborenen und Säuglingen auftretende Nephrose eigenen Gepräges zu unterscheiden begonnen: das kongenitale nephrotische Syndrom. Diese Krankheit kommt in Finnland weit häufiger als anderswo vor, weshalb sie dort besonders reges Interesse erweckt hat. In der Kinderklinik der Universität Helsinki ist versucht worden, die Krankheit von den verschiedensten Seiten her zu erforschen. Die vorliegende Arbeit hat den Zweck, einerseits die vorhandene Literatur zusammenzufassen und andererseits die besonders in Finnland gewonnenen Erfahrungen zu veröffentlichen, was in dieser umfassenden Weise bisher noch nicht geschehen ist. So monoton das Krankheitsbild des kongenitalen nephrotischen Syndroms in Finnland auftritt, so sind in anderen Ländern zwar ähnliche, aber doch auch beträchtlich abweichende Fälle beschrieben worden, deren ätiologische Übereinstimmung mit der finnischen Krankheit nicht ohne weiteres klar ist. Sofern nicht anders angegeben, sprechen wir im vorliegenden Text vom kongenitalen nephrotischen Syndrom auf Grund der in Finnland gemachten Erfahrungen.

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Copyright information

© Springer-Verlag, Berlin · Heidelberg 1970

Authors and Affiliations

  1. 1.Universitäts-KinderklinikHelsinki 29Finnland

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