Anomalies of the Aortic Arch with Compression of the Trachea or Esophagus

  • G. Ekström


Many vascular anomalies may occur in the superior mediastinum, since the embryonic development of the aortic system, the pulmonary artery and the ductus arteriosus is highly complex. Parts of the branchial arch arteries which normally involute and disappear may persist, and vice versa. The final result may thus be a mirror image of the normal, which can be described as a strictly localized vascular transposition. Occasionally the primitive bifid arch of the aorta persists, forming a “double aortic arch” which encircles the trachea and esophagus. Parts of such a vascular ring may be obliterated and form fibrous bands while the rest of the ring remains patent. Or some of the ring may completely regress, leaving a horseshoe-shaped portion.


Aortic Arch Club Foot Left Subclavian Artery Branchial Arch Vascular Ring 
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  • G. Ekström

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