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Radionuclide Evaluation of Pharyngeal Emptying Before and After Cricopharyngeal Myotomy in Patients with Oculopharyngeal Muscular Dystrophy

  • R. Taillefer
  • G. Beauchamp
  • A. Duranceau
Conference paper

Abstract

Oculopharyngeal muscular dystrophy (OMD) is a genetic condition transmitted with an autosomal dominant mode. It is characterized by a bilateral symmetrical ptosis with progressive oropharyngeal dysphagia occurring late in life (Duranceau et al. 1983). Motility studies have revealed an impaired pharyngeal function with weak and slow contractions. The unrelaxed or incompletely relaxed upper esophageal sphincter (UES) makes it a functional obstruction against the powerless pharynx. The goal of the treatment is to facilitate the passage of food from the pharynx to the cervical esophagus, across the UES. No medication provides significant help for that purpose and dilatation does not result in satisfactory long-term improvement (Duranceau et al. 1978). Cricopharyngeal myotomy remains the best approach to enhance the pharyngeal clearance of a food bolus (Peterman et al. 1964).

Keywords

Oropharyngeal Dysphagia Pyriform Sinus Autosomal Dominant Mode Liquid Bolus Cricopharyngeal Myotomy 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag 1988

Authors and Affiliations

  • R. Taillefer
    • 1
  • G. Beauchamp
    • 1
  • A. Duranceau
    • 1
  1. 1.Hôpital Hôtel-Dieu de MontréalUniversité de MontréalMontréalCanada

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