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Rhabdomyosarcoma

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Cancer in Children

Part of the book series: UICC International Union Against Cancer ((1360))

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Abstract

Rhabdomyosarcoma (RMS) is a tumour that may arise in any part of the body where striated muscle is found. It is the most common soft-tissue tumour in childhood and represents 8% of all malignant diseases in children under 15 years [1]. It is clearly distinct from other soft-tissue sarcomas (discussed in Chap. 26, this volume). The incidence of RMS shows two peaks: an early one between ages 1 and 7 years and a second one during adolescence (Fig. 1) [2]. The median age at diagnosis is 5 years in studies carried out by the International Society of Paediatric Oncology (SIOP). There is a higher incidence among males (sex ratio 1.7).

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Authors
  1. F. Flamant
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  2. P. A. Voûte
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  3. D. Sommelet
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Editor information

Editors and Affiliations

  1. Department of Paediatric Oncology, Emma Kinderziekenhuis, Div. of Paediatrics Academic Medical Center, Meibergdreef 9, rm F8-239, 1105 AZ, Amsterdam, The Netherlands

    P. A. Voûte

  2. Department of Radiation Oncology, Beatson Oncology Centre, Western Infirmary, G11 6NT, Glasgow, UK

    Ann Barrett

  3. Service de Pédiatrie, Institut Gustave Roussy, Rue Camille Desmoulins, F-94805, Villejuif Cedex, France

    Jean Lemerle

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© 1992 Springer-Verlag Berlin Heidelberg

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Flamant, F., Voûte, P.A., Sommelet, D. (1992). Rhabdomyosarcoma. In: Voûte, P.A., Barrett, A., Lemerle, J. (eds) Cancer in Children. UICC International Union Against Cancer. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-84722-6_25

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  • DOI: https://doi.org/10.1007/978-3-642-84722-6_25

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-84724-0

  • Online ISBN: 978-3-642-84722-6

  • eBook Packages: Springer Book Archive

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