Langerhans Cell Histiocytosis

  • Kenneth L. McClain
  • John J. Hutter
  • J. Robert Cassady
Part of the Medical Radiology book series (MEDRAD)


A panel of experts representing the Histiocyte Society has suggested that the original terminology for the various syndromes in the “histiocytosis X” category (eosinophilic granuloma, Letterer-Siwe disease, and Hand-Christian-Schüller syndrome) be discarded and replaced by the term Langerhans cell histiocytosis (LCH) (Chu et al. 1987). This is because the proliferative cell which causes these entities is known to be the Langerhans cell.


Diabetes Insipidus Growth Hormone Deficiency Eosinophilic Granuloma Juvenile Xanthogranuloma Histiocyte Society 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer-Verlag Berlin Heidelberg 1994

Authors and Affiliations

  • Kenneth L. McClain
    • 1
  • John J. Hutter
    • 2
  • J. Robert Cassady
    • 3
  1. 1.Department of Pediatrics, Baylor College of MedicineTexas Childern’s HospitalHoustonUSA
  2. 2.Department of Pediatrics, Arizona Health Sciences CenterUniversity of ArizonaTucsonUSA
  3. 3.Department of Radiation OncologyThe University of Arizona, Health Sciences CenterTucsonUSA

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