Abstract
A panel of experts representing the Histiocyte Society has suggested that the original terminology for the various syndromes in the “histiocytosis X” category (eosinophilic granuloma, Letterer-Siwe disease, and Hand-Christian-Schüller syndrome) be discarded and replaced by the term Langerhans cell histiocytosis (LCH) (Chu et al. 1987). This is because the proliferative cell which causes these entities is known to be the Langerhans cell.
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McClain, K.L., Hutter, J.J., Cassady, J.R. (1994). Langerhans Cell Histiocytosis. In: Cassady, J.R. (eds) Radiation Therapy in Pediatric Oncology. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-84520-8_22
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