Scoliosis and its Treatment in the Prader-Willi Syndrome

  • Mel W. Jones
Conference paper
Part of the NATO ASI Series book series (volume 61)

Abstract

Scoliosis in Prader-Willi Syndrome (PWS) was first noted by Laurance (1967) who thought it was a common feature of the Syndrome since it was also present in a number of patients referred by pediatric colleagues. It may to be due to hypotonia (Zellweger and Schneider, 1968). The reported prevalence rates vary widely from 7% (Zellweger and Schneider, 1968) to 97% (Holm and Laurnen, 1981). The latter emphasised that clinical examination alone is not reliable in detecting scoliosis in these short and obese children. In their series of 37, all of whom had spine radiographs, 36 (97%) had scoliosis. However, most were not severe. Only 5 (14%) had a scoliosis over 20 degrees, and only one patient underwent surgery.

Keywords

Obesity Osteoporosis Neurol Meningitis Thrombocytopenia 

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Copyright information

© Springer-Verlag Berlin Heidelberg 1992

Authors and Affiliations

  • Mel W. Jones
    • 1
  1. 1.University Department of Orthopaedic SurgeryGlenfield General HospitalEngland

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