Electrophysiologic Studies in Patients with Hypertrophic Cardiomyopathy: Safety and Relation of Results to Clinical Findings

  • L. Fananapazir


Patients with hypertrophic cardiomyopathy have a varied clinical presentation. This includes symptoms that suggest an arrhythmic etiology: sudden cardiac arrest, syncope, presyncope, and palpitations. Since early studies linked ventricular tachycardia recorded during Holter monitoring with subsequent sudden cardiac death [1–3], many asymptomatic hypertrophic cardiomyopathy patients are also referred for evaluation due to the presence of ventricular tachycardia (most nonsustained) during 24–48 h Holter monitoring. Electrophysiologic studies have an established role in elucidating possible arrhythmic cause of sudden cardiac arrest, syncope and palpitation and guiding therapy in many other cardiac disease states. Programmed electrical stimulation in hypertrophic cardiomyopathy patients has unfortunately resulted in death in isolated patients [4, 5] and programmed ventricular stimulation has been reported to result in the induction of non-specific ventricular arrhythmias.


Ventricular Tachycardia Ventricular Arrhythmia Hypertrophic Cardiomyopathy Sudden Cardiac Arrest Polymorphic Ventricular Tachycardia 
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© Springer-Verlag Berlin Heidelberg 1990

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  • L. Fananapazir

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