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Cardiac Involvement in Kearns-Sayre Syndrome

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Heart & Brain, Brain & Heart

Abstract

Progressive external ophthalmoplegia (PEO) is accompanied by a progressive weakness of the external muscles of the eyes. It was first described by Albrecht von Graefe in 1866 [20]. First believed to be of neurogenic origin, it was not until 1951 that Kiloh and Nevin [30] suggested that the ocular signs were due to a myopathy as they in one case found histological abnormalities in the medial rectus muscle.

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Authors
  1. B. Schwartzkopff
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  2. G. Breithardt
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  3. M. Borggrefe
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  4. B. Lösse
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  5. K.-V. Toyka
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  6. H. Frenzel
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Editor information

Editors and Affiliations

  1. Department of Physiology Institute of Medical Biology, University of Tromsø, Tromsø, Norway

    Helge Refsum

  2. Department of Neurology Institute of Clinical Medicine, University of Tromsø, Tromsø, Norway

    Ilmar A. Sulg

  3. Section of Cardiology Department of Internal Medicine, University of Tromsø, Tromsø, Norway

    Knut Rasmussen

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© 1989 Springer-Verlag Berlin Heidelberg

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Schwartzkopff, B., Breithardt, G., Borggrefe, M., Lösse, B., Toyka, KV., Frenzel, H. (1989). Cardiac Involvement in Kearns-Sayre Syndrome. In: Refsum, H., Sulg, I.A., Rasmussen, K. (eds) Heart & Brain, Brain & Heart. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-83456-1_25

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  • DOI: https://doi.org/10.1007/978-3-642-83456-1_25

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-83458-5

  • Online ISBN: 978-3-642-83456-1

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