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27. Hämophilie-Symposion Hamburg 1996 pp 330–339Cite as

Acquired von Willebrand Disease in Monoclonal Gammapathies: Effectiveness of High-Dose Intravenous Gammaglobulin

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Zusammenfassung

Acquired von Willebrand disease (AvWD) is a bleeding disorder strikingly similar to congenital von Willebrand disease in terms of clinical manifestations and laboratory findings being characterized by a prolonged bleeding time and low levels of factor VIII von Willebrand factor (FVIII/vWf) complex, but without a family history of a congenital bleeding tendency and absence of abnormal bleeding after hemostatic challenges.

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References

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Authors
  1. J. J. Michiels
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Editors and Affiliations

  1. Zentr. d. Inn. Med., Med. Klinik I, Universitätsklinikum, Theodor-Stern-Kai 7, D-60590, Frankfurt am Main, Deutschland

    Inge Scharrer

  2. Hämostaseologische Abteilung, Med. Univ.-Klinik Innenstadt, Ziemssenstraße 1a, D-80336, München, Deutschland

    Wolfgang Schramm

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© 1998 Springer-Verlag Berlin Heidelberg

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Michiels, J.J. (1998). Acquired von Willebrand Disease in Monoclonal Gammapathies: Effectiveness of High-Dose Intravenous Gammaglobulin. In: Scharrer, I., Schramm, W. (eds) 27. Hämophilie-Symposion Hamburg 1996. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-80403-8_50

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  • DOI: https://doi.org/10.1007/978-3-642-80403-8_50

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-62915-3

  • Online ISBN: 978-3-642-80403-8

  • eBook Packages: Springer Book Archive

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