Urinary System pp 310-313 | Cite as

Nephronophthisis, Mouse

  • James D. Fikes
Part of the Monographs on Pathology of Laboratory Animals book series (LABORATORY)


Nephronophthisis is an inherited progressive nephropathy of CBA/CaH-kd (also called kdkd) mice that results in an atypical end-stage kidney disease characterized by massively dilatated tubules, mononuclear interstitial infiltrate, and minimal interstitial fibrosis.


Kidney disease of mice 


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© Springer-Verlag Berlin Heidelberg 1998

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  • James D. Fikes

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