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Primär genetische Hyperlipoproteinämien im Kindesalter

  • B. Koletzko
Conference paper

Zusammenfassung

Das Behandlungsziel bei Kindern und Jugendlichen mit primär genetischen Hyperlipoproteinämien ist die Langzeitprävention sekundärer Organschäden mit geringstmöglichem Nebenwirkungsrisiko. Dabei ist für die große Mehrzahl der Patienten eine konsequente Modifikation der Ernährung die grundlegende und wichtigste Therapiemaßnahme [25, 29]. Medikamentöse Lipidsenker werden bei pädiatrischen Patienten zurückhaltend und nur bei strenger Indikation eingesetzt, ihre Anwendung erfolgt stets ergänzend zu einer Diättherapie [27, 30, 50]. In diesem Beitrag werden ernährungstherapeutische Aspekte der im Kindesalter praktisch wichtigen schweren Hyperlipoproteinämieformen diskutiert.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1993

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  • B. Koletzko

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