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Bone Marrow Transplantation in the Treatment of Congenital T Cell Disorders

  • W. Friedrich
  • C. Knobloch
  • W. Hartmann
Conference paper

Abstract

Bone marrow transplantation (BMT) plays a central role in the management of congenital immunodeficiencies characterized by profound abnormalities of the T cell system [10, 14, 19]. This heterogeneous group of disorders may be corrected by the establishment of a new, donor-dependent immmune system. BMT in these disorders also represents a unique model to study and to define cellular interactions which are operative in the functional reconstitution of the lymphohemopoietic system in man.

Keywords

Bone Marrow Transplantation Severe Combine Immunodeficiency Primary Immunodeficiency Disease Adenosine Deaminase Deficiency Congenital Immunodeficiency 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1993

Authors and Affiliations

  • W. Friedrich
  • C. Knobloch
  • W. Hartmann

There are no affiliations available

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