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Desmoids in Gardner’s Syndrome: A Challenge for Surgeons

  • S. Martinoli
  • L. Mariani
  • A. Goldhirsch
Conference paper
Part of the ESO Monographs book series (ESO MONOGRAPHS)

Abstract

Gardner’s first description [1] of the association of familial adenomatous polyposis (FAP) with osteomas and skin lesions (1951–1953) was followed by steadily increasing discoveries of other extracolonic manifestations, such as upper gastrointestinal lesions (fundic gland polyps, true gastric and duodenal adenomas) [2], desmoid tumours, retinal changes and other more unusual associations like brain tumours [3], papillary carcinoma in the thyroid [4] and hepatoblastomas [5].

Keywords

Familial Adenomatous Polyposis Brachial Plexus Papillary Carcinoma Desmoid Tumor Familial Polyposis 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Berlin Heidelberg 1992

Authors and Affiliations

  • S. Martinoli
    • 1
  • L. Mariani
    • 1
  • A. Goldhirsch
    • 1
  1. 1.Department of Surgery and Division of OncologyOspedale CivicoLuganoSwitzerland

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