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Fibrous Tumors and Tumor-like Lesions of Childhood: Diagnosis, Differential Diagnosis, and Prognosis

  • Chapter
Soft Tissue Tumors

Part of the book series: Current Topics in Pathology ((CT PATHOLOGY,volume 89))

Abstract

The most important group of lesions among the fibrous tumors of childhood are the fibromatoses. These are rare, non-metastasizing (myo-)fibroblastic tumor-like lesions of unknown etiology with the following characteristic features:

  1. 1.

    They tend to invade the surrounding tissue more or less aggressively.

  2. 2.

    They tend to recur after incomplete excision.

  3. 3.

    Some types may regress spontaneously, and regression may be complicated by contraction.

  4. 4.

    They never metastasize.

  5. 5.

    Certain fibromatoses may be either solitary or multiple.

  6. 6.

    Most types occur in very young age groups and can appear as congenital tumors.

  7. 7.

    The biologic behavior, particularly the risk of recurrences, correlates partially with the histological subtype, i.e., some fibromatoses tend to recur only rarely, while others, especially desmoid-type fibromatoses, show high recurrence rates.

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Authors
  1. D. Schmidt
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Editor information

Editors and Affiliations

  1. Institut für Paidopathologie, Klinikum der Christian-Albrechts-Universität, Michaelisstr. 11, 24105, Kiel, Germany

    D. Harms Professor Dr.

  2. Institut für Pathologie, A2,2, 68159, Mannheim, Germany

    D. Schmidt Professor Dr.

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© 1995 Springer-Verlag Berlin Heidelberg

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Schmidt, D. (1995). Fibrous Tumors and Tumor-like Lesions of Childhood: Diagnosis, Differential Diagnosis, and Prognosis. In: Harms, D., Schmidt, D. (eds) Soft Tissue Tumors. Current Topics in Pathology, vol 89. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-77289-4_9

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  • DOI: https://doi.org/10.1007/978-3-642-77289-4_9

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-77291-7

  • Online ISBN: 978-3-642-77289-4

  • eBook Packages: Springer Book Archive

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