Malignant Peripheral Neuroectodermal Tumor

  • D. Schmidt
Part of the Current Topics in Pathology book series (CT PATHOLOGY, volume 89)


Primitive neuroectodermal tumors (PNETs) constitute a diverse group of small cell neoplasms which may occur in the central nervous system and in peripheral sites including the soft tissues and bone. Accordingly, they have been subdivided into central and peripheral PNETs. The revised classification system of the World Health Organization (WHO) on pediatric brain tumors by Rorke et al. (1985) provoked a continuous discussion on the former group of tumors with some principal investigators deeming it a too simplistic scheme and favoring the retention of the conventional classification system (Rubinstein 1987).


Neural Differentiation Neuroectodermal Tumor Primitive Neuroectodermal Tumor Small Round Cell Tumor Olfactory Neuroblastoma 
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© Springer-Verlag Berlin Heidelberg 1995

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  • D. Schmidt

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