Isolated Angiitis of the Central Nervous System

  • Patricia M. Moore


Isolated angiitis of the CNS (IAC) is an idiopathic, recurrent vasculitis restricted to small and medium-sized vessels of the brain and spinal cord. Early reports were based on autopsy cases, but the disease is now increasingly recognized and treated ante mortem. Initially the disease was called “granulomatous angiitis” [2, 5, 6, 8, 10, 11] but the term “isolated angiitis” is preferable because it emphasizes the location of the vasculitis rather than a variable histologic finding. The true incidence is unknown, but the disease is not as rare as previously thought.


Herpes Zoster Retinal Vasculitis Chronic Meningitis Left Atrial Myxoma Granulomatous Angiitis 
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© Springer-Verlag Berlin Heidelberg 1993

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  • Patricia M. Moore

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