Human Cytochrome c Oxidase Deficiencies; Structural and Functional Aspects

  • K. M. C. Sinjorgo
  • A. O. Muijsers
  • H. R. Scholte
  • A. B. P. Van Kuilenburg
  • J. J. Vanbeeumen
  • E. M. Brouwer-Kelder
  • J. A. Berden
  • P. A. Bolhuis
  • J. M. Tager

Abstract

Mitochondria play a key role in aerobic energy metabolism in eukaryotic cells. The main function of the organelles is the oxidation of fuel molecules by oxygen and the concomitant energy production in the form of ATP.

Keywords

Polypeptide Neurol NADH Nucleoside Triphosphate 

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Copyright information

© Springer-Verlag Berlin Heidelberg 1989

Authors and Affiliations

  • K. M. C. Sinjorgo
    • 1
  • A. O. Muijsers
    • 1
  • H. R. Scholte
    • 2
  • A. B. P. Van Kuilenburg
    • 1
  • J. J. Vanbeeumen
    • 3
  • E. M. Brouwer-Kelder
    • 1
  • J. A. Berden
    • 1
  • P. A. Bolhuis
    • 4
  • J. M. Tager
    • 1
  1. 1.laboratory of BiochemistryUniversity of AmsterdamAmsterdamThe Netherlands
  2. 2.Department of Biochemistry IErasmus University RotterdamThe Netherlands
  3. 3.Laboratory of Microbiology and Microbial GeneticsUniversity of GhentBelgium
  4. 4.Department of NeurologyUniversity of Amsterdam, Academic Medical CentreThe Netherlands

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