Human Cytochrome c Oxidase Deficiencies; Structural and Functional Aspects

  • K. M. C. Sinjorgo
  • A. O. Muijsers
  • H. R. Scholte
  • A. B. P. Van Kuilenburg
  • J. J. Vanbeeumen
  • E. M. Brouwer-Kelder
  • J. A. Berden
  • P. A. Bolhuis
  • J. M. Tager


Mitochondria play a key role in aerobic energy metabolism in eukaryotic cells. The main function of the organelles is the oxidation of fuel molecules by oxygen and the concomitant energy production in the form of ATP.


Mitochondrial Myopathy Human Cytochrome Oxidase Deficiency Chronic Progressive External Ophthalmoplegia Mammalian Cytochrome 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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© Springer-Verlag Berlin Heidelberg 1989

Authors and Affiliations

  • K. M. C. Sinjorgo
    • 1
  • A. O. Muijsers
    • 1
  • H. R. Scholte
    • 2
  • A. B. P. Van Kuilenburg
    • 1
  • J. J. Vanbeeumen
    • 3
  • E. M. Brouwer-Kelder
    • 1
  • J. A. Berden
    • 1
  • P. A. Bolhuis
    • 4
  • J. M. Tager
    • 1
  1. 1.laboratory of BiochemistryUniversity of AmsterdamAmsterdamThe Netherlands
  2. 2.Department of Biochemistry IErasmus University RotterdamThe Netherlands
  3. 3.Laboratory of Microbiology and Microbial GeneticsUniversity of GhentBelgium
  4. 4.Department of NeurologyUniversity of Amsterdam, Academic Medical CentreThe Netherlands

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