Compression of the Cervical Spinal Cord in Mucopolysacharidosis
A 39-year-old man suffering from mucopolysacharidosis type II (Runter disease) developed cervical myelopathy mainly with disturbance of gait. CT and myelography showed an important hyperdense enlargement of the dura with severe compression of the spinal cord and the surrounding subarachnoid space from the foramen magnum to the levai of C5. For decompression, laminectomy C1–C3 and durai splitting with plastic reconstruction was performed. The patient improved for 1 month following operation and has now been stable for 2 years.