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Not an Ichthyosis at All: the Keratitis, Ichthyosis-like Hyperkeratosis, and Deafness (KID) Syndrome

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The Ichthyoses

Abstract

In 1915, the American dermatologist Frederick S.Burns [3] delineated the keratitis, ichthyosis-like hyperkeratosis, and deafness (KID) syndrome in full detail. He described a 16-year-old boy who was partially blind, totally deaf, and displayed a peculiar type of hyperkeratotic involvement localized to the head and the limbs with bizarre, sharply outlined lesions over the face. The disease had started at the age of 1 year and progressed until the age of about 10 years. During the following years the conditions remained unchanged. Though Burns presented his case at the 38th Meeting of the American Dermatological Association in May 1914, the syndrome he described soon fell into oblivion.

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Authors and Affiliations

  1. Department of Human Genetics, University of Nijmegen, Geert Grooteplein zuid 20, NL-6500, HB Nijmegen, The Netherlands

    Priv. Doz. Dr. Heiko Traupe

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  1. Priv. Doz. Dr. Heiko Traupe
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© 1989 Springer-Verlag Berlin Heidelberg

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Traupe, H. (1989). Not an Ichthyosis at All: the Keratitis, Ichthyosis-like Hyperkeratosis, and Deafness (KID) Syndrome. In: The Ichthyoses. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-73650-6_21

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  • DOI: https://doi.org/10.1007/978-3-642-73650-6_21

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-73652-0

  • Online ISBN: 978-3-642-73650-6

  • eBook Packages: Springer Book Archive

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