Anästhesie bei Kindern mit Duchenne-Muskeldystrophie

  • H. Huttarsch
Conference paper
Part of the Kinderanästhesie book series (KINDERANAESTHES)


Die Duchenne-Muskeldystrophie (DMD), eine primär degenerative erbliche Muskelerkrankung, ist mit 2/3 aller Fälle die am häufigsten vorkommende Muskeldystrophie. Etwa 75 Neugeborene sind pro Jahr in der Bundesrepublik betroffen. In etwa 1/3 der Erkrankungsfälle sind Neumutationen die Ursache. Der Erbgang ist X-Chromosomal rezessiv, d. h. es erkranken nur Knaben (von wenigen Ausnahmen abgesehen).


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© Springer-Verlag Berlin Heidelberg 1989

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  • H. Huttarsch

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