Abstract
Idiopathic juvenile osteoporosis (IJO) occurs sporadically between the age of 6 and 15 years. It manifests itself as a high-grade, progressive osteopenia accompanied by bone pain. Secondarily, fractures and bowing of the tubular bones occur. Radiologically, osteopenia is particularly marked in the vertebral column (fig. 1). As a result, a very marked lumbodorsal kyphoscoliosis develops. Further characteristic features are sub-meta-physeal fractures of the long tubular bones. To date, genetic determination is unknown. In late adolescence, progression of IJO is halted. The further prognosis and the quality of the patient’s life depend upon the skeletal deformations that have occured within the intervening period. Differential-diagnostically, consideration must first be given to osteogenesis imperfecta (OI) and unclassifiable osteopenias of childhood.
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© 1987 Springer-Verlag Berlin Heidelberg
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Stöß, H., Pontz, B.F., Karbowski, A., Pesch, HJ. (1987). Idiopathic Juvenile Osteoporosis — Light- and Electronmicroscopic Findings in the Iliac Crest. In: Kuhlencordt, F., Dietsch, P., Keck, E., Kruse, HP. (eds) Generalized Bone Diseases. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-73346-8_4
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DOI: https://doi.org/10.1007/978-3-642-73346-8_4
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