Congenital Arterial and Arteriovenous Dysplasia

  • R. J. A. M. van Dongen


Angiodysplasias are a combination of several different congenital malformations. They are polydysplasias with arterial, venous, capillary, and lymphatic components. Pathologic changes involve not only the vascular systems, but all other tissues as well: skin, connective tissues, bones, cartilage, and nerves. The classification of the different clinical pictures is based mainly on the vascular system predominant in each type of angiodysplasia [10,11,13,16,19]. The treatment of angiodysplastic anomalies is sometimes palliative, symptomatic, or cosmetic (reduction of the difference in length between the limbs, surgery of varices, extirpation of hemangiomas, lymphangiomas, and other vascular and connective tissue proliferations localized on the body’s surface). Most therapeutic measures are focused on the arterial components of the anomaly, on arterial hypervascularization, vascular proliferations, and especially on pathologic arteriovenous shunts. The aim of treatment is not only to eliminate active arteriovenous fistulas and vascular proliferations by resecting and inducing obliteration, but also to minimize hypervascularization. These therapeutic measures are not suited to angiodysplastic changes that are limited to the venous system.


Arteriovenous Fistula Internal Iliac Artery Fibrin Seal External Iliac Artery Arteriovenous Shunt 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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  1. 1.
    van Dongen RJAM (1983) Therapie der angeborenen arteriövenosen Angiodysplasien unter besonderer Berücksichtigung der operativen Embolisation. Angio 5:169Google Scholar
  2. 2.
    van Dongen RJAM (1985) Angeborene arterio-venöse Dysplasie: Behandlungsindikation, angiographische Dokumentation, kombinierte percutane und operative Behandlung. Chirurg 56:65PubMedGoogle Scholar
  3. 3.
    Ehrenfeld WK (1976) Diskussionsbemerkung. Surgery 79:11Google Scholar
  4. 4.
    Elliot JP Jr, Hageman JH, Szilagyi E, Ramakrishnan V, Bravo JJ, Smith RF (1980) Arterial embolization. Problems of source, multiplicity, recurrence, and delayed treatment. Surgery 88:833Google Scholar
  5. 5.
    Florack G, Sandmann W, Müller H, Lerut J, Kremer K (1980) Arteriovenöse Fisteln- Mögliehkeiten und Grenzen der operativen Behandlung. Angio 2:47Google Scholar
  6. 6.
    Frileux C, Blonstein A (1976) Embolisation thera-peutique pour anévrisme cirsoide récidive de la main. J Mai Vase 1:47Google Scholar
  7. 7.
    Grace DM, Pitt DF, Gold RE (1976) Vascular embolization and occlusion by angiographic techniques as an aid or alternative to operation. Surg Gynecol Obstet 143:469PubMedGoogle Scholar
  8. 8.
    Joyce PF, Sundaram M, Afzal Riaz M, Wolverson MK, Barner HB, Hoffmann RJ (1980) Embolisation of extensive peripheral angiodysplasias. Arch Surg 115:665PubMedCrossRefGoogle Scholar
  9. 9.
    Konrad EA, Stiegler H, Meister P, Becker HM (1980) Das P.F. Weber-Syndrom; Umschriebener Riesenwuchs der unteren Extremität mit kongenitalen arteriovenösen Fisteln. Vasa 9:331PubMedGoogle Scholar
  10. 10.
    Malan E, Puglionisi A (1964) Congenital angiodysplasias of the extremities; generality and classification; venous dysplasias. J Cardiovasc Surg 5:87Google Scholar
  11. 11.
    Malan E, Puglionisi A (1965) Congenital angiodysplasias of the extremities; arterial, arterial and venous, and haemolymphastic dysplasias. J Cardiovasc Surg 6:255Google Scholar
  12. 12.
    Malan E (1965) Surgical problems in the treatment of congenital arteriovenous fistulae. J Cardiovasc Surg [Suppl]: 251Google Scholar
  13. 13.
    May R, Nissl R (1970) Beitrag zur Klassifizierung der „gemischten Angiodysplasien“. ROFO 113:170CrossRefGoogle Scholar
  14. 14.
    Natali J, Merland J J (1976) Superselective arteriography and therapeutic embolisation for vascular malformations (angiodysplasias). J Cardiovasc Surg 17:465Google Scholar
  15. 15.
    Olcott C, Newton TH, Stoney RJ, Ehrenfeld WK (1976) Intra-arterial embolization in the management of arteriovenous malformations. Surgery 79:3PubMedGoogle Scholar
  16. 16.
    Pratesi F (1972) Classification of angiopathic diseases of the limbs. Folia Angiologica 20:193Google Scholar
  17. 17.
    Rickets RR, Finck E, Yellin AE (1978) Management of major arteriovenous fistulas by arteriographic techniques. Arch Surg 113:1153CrossRefGoogle Scholar
  18. 18.
    Stillman RM, Powers JC, Fitzgerald JF (1977) Cosmetic excision of an isolated extracranial arteriovenous malformation using Gelfoam embolization. Br J Surg 64:784PubMedCrossRefGoogle Scholar
  19. 19.
    Vollmar JF (1974) Zur Geschichte und Terminologie der Syndrome nach F.P. Weber und Klippel-Treaunay. Vasa 3:321Google Scholar
  20. 20.
    Vollmar JF, Stalker CG (1976) The surgical treatment of congenital arteriovenous fistulas in the extremities. J Cardiovasc Surg 17:340Google Scholar

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© Springer-Verlag Berlin Heidelberg 1989

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  • R. J. A. M. van Dongen

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