Advertisement

Das Prune-Belly-Syndrom

  • B. H. Belohradsky
  • C. Henkel
Conference paper
  • 13 Downloads
Part of the Ergebnisse der Inneren Medizin und Kinderheilkunde/Advances in Internal Medicine and Pediatrics book series (KINDERHEILK. NF, volume 52)

Zusammenfassung

Das Prune-Belly-Syndrom (PBS) ist eine angeborene Mißbildungserkrankung, die ganz überwiegend beim männlichen Geschlecht vorkommt. Charakteristisch ist die Symptomtrias Bauchmuskelaplasie, total oder partiell, bzw. Bauchmuskelhypoplasie, Anomalien der Harnorgane und Kryptorchismus.

Key words

Pathogenese Prune-Belly Syndrom Bauchmuskelaplasie Harnwegsmißbildungen Kryptorchismus Embryologie Literaturübersicht Prognose Therapie Altersverteilung 

Preview

Unable to display preview. Download preview PDF.

Unable to display preview. Download preview PDF.

Literatur

  1. 1.
    Adeyokunnu AA, Adeniyi A, Kolawoli TM, Nkposong EO (1975) Prune belly syndrome. A study of ten cases in Nigerian children with common and uncommon manifestations. East Afr Med J 52:438PubMedGoogle Scholar
  2. 2.
    Afifi AK, Rebeiz J, Mire J, Andonian SJ, Der Kaloustian VM (1972) The myopathology of the prune belly syndrome. J Neurol Sci 15:153PubMedCrossRefGoogle Scholar
  3. 3.
    Alford BA, Peoples WM, Resnick JS, L’Heureux PR (1978) Pulmonary complications associated with the prune belly syndrome. Pediatr Radiol 129:401Google Scholar
  4. 4.
    Altshuler G (1973) Cytomegalovirus and biliary atresia. Lancet 2:1206PubMedCrossRefGoogle Scholar
  5. 5.
    Andrén L, Bjersing L, Lagergren J (1964) Congenital aplasia of the abdominal muscles with urogenital malformations. Acta Radiol Diagn (Stockh) 2:298Google Scholar
  6. 6.
    Arena JFP, Smith DW (1978) Sex liability to single structural defects. Am J Dis Child 132:970PubMedGoogle Scholar
  7. 7.
    Asplund J, Laska J (1975) Prune belly syndrome at the age of 37. Case report. Scand J Urol Nephrol 9:297PubMedCrossRefGoogle Scholar
  8. 8.
    Barnhouse DH (1972) Prune belly syndrome. Br J Urol 44:356PubMedCrossRefGoogle Scholar
  9. 9.
    Becroft MO (1979) Prenatal cytomegalovirus infection anal muscular deficiency (eventration) of the diaphragm. J Pediatr 94:74PubMedCrossRefGoogle Scholar
  10. 10.
    Benirschke K, Mendoza GR, Bazeley PL (1974) Placental and fetal manifestations of cytomegalovirus infection. Virchows Arch (Cell Pathol 16:121CrossRefGoogle Scholar
  11. 11.
    Benyesh-Melnick M, Rosenberg HS, Watson B (1964) Viruses in cell cultures of kidneys of children with congenital heart malformations and other diseases. Proc Soc Wxp Biol Med 117:452Google Scholar
  12. 12.
    Berenberg W, Nankervis G (1970) Long-term follow-up of cytomegalic inclusion disease of infancy. Pediatrics 46:403PubMedGoogle Scholar
  13. 13.
    Bilger M, Hatemi N, Ilter Ö, Tümay SB (1968) Aplasie congénitale de la musculature abdominale associée à certaines malformations urogénitales. Pédiatrie 23:571PubMedGoogle Scholar
  14. 14.
    Blattner RJ, Williamson AP, Heys FM (1973) Role of viruses in the etiology of congenital malformations. Progr Med Virol 15:1Google Scholar
  15. 15.
    Boissonnat P, Duhamel B (1962) Congenital diverticulum of the anterior urethra associated with aplasia of the abdominal muscles in a male infant. Br J Urol 34:59PubMedCrossRefGoogle Scholar
  16. 16.
    Bourne CW, Cerny JC (1967) Congenital absence of abdominal muscles: Report of 6 cases. J Urol 98:252PubMedGoogle Scholar
  17. 17.
    Bozic C (1974) Ectopic fetal adrenal cortex in the lung of a newborn. Virchows Arch (Pathol Anat) 363:371CrossRefGoogle Scholar
  18. 18.
    Braun-Falco O, Rupec M, Lindley MJ (1964) Angeborene Dermatochalasis als Leitsymptom eines Symptomenkomplexes. Eine klinische, licht-und elektronenmikroskopische Studie. Arch Klin Exp Dermatol 220:166PubMedCrossRefGoogle Scholar
  19. 19.
    Brierre JT (1963) Congenital abnormalities of the genito-urinary tract: Abdominal muscle dysplasia and choanal atresia. Pediatrics 31:290PubMedGoogle Scholar
  20. 20.
    Bronzini E, Miscatelli P (1973) L’aplasia della musculatura della parete abdominale associata a malformazioni genito-urinarie in due fratellin. Pathologica 65:127PubMedGoogle Scholar
  21. 21.
    Burke EC, Shin MH, Kelalis PP (1969) Prune belly syndrome. Clinical findings and survival. Am J Dis Child 117:668PubMedGoogle Scholar
  22. 22.
    Burkholder GV, Harper RC, Beach PD (1970) Congenital absence of the abdominal muscles: A clinicopathologic correlation. Am J Clin Pathol 53:602PubMedGoogle Scholar
  23. 23.
    Carter TC, Timskey GC, Ozog LS (1974) Prune belly syndrome. Review of ten cases. Urology 3:279PubMedCrossRefGoogle Scholar
  24. 24.
    Ceccarelli FE (1973) Combined transpyeloureterostomy and ipsilateral pyeloureterostomy and orchiopexy by testicular artery transection: Treatment in a case of prune belly syndrome. J Urol 110:596PubMedGoogle Scholar
  25. 25.
    Cenani A, Tümy G, Eginel A (1978) Das prune belly Syndrom mit Meningomyelocele — ein „neues Syndrom”? Monatsschr Kinderheilkd 126:287PubMedGoogle Scholar
  26. 26.
    Chesney RW, Rogers SE (1976) Salt-losing nephropathy in prune belly syndrome: Reversal following unilateral nephrectomy. Am J Dis Child 130:778PubMedGoogle Scholar
  27. 27.
    Cinque NA, Rosso C (1964) Un raro caso di ipoplasia della muscolatura addominale associato a malformazioni genito-urinarie e cardiache. Minerva Pediatr 16:771PubMedGoogle Scholar
  28. 28.
    Coppola G, Varcasia E (1957) Considerazioni anatomo cliniche a patogenetiche su di un caso di agenesia completa dei muscoli abdominali anteriori associata ad alterazioni delle vie urinarie. Minerva Pediatr 9:1156PubMedGoogle Scholar
  29. 29.
    Cremin J (1971) The urinary tract anomalies associated with agenesis of abdominal walls. Br J Radiol 44:767PubMedCrossRefGoogle Scholar
  30. 30.
    Crome L, France NE (1959) Microgyria and cytomegalic inclusion disease in infancy. J Clin Pathol 12:427PubMedCrossRefGoogle Scholar
  31. 31.
    Cugier J (1977) Resection of the urethra with the prune belly syndrome. Birth Defects 13:95Google Scholar
  32. 32.
    D’Attoma G (1975) La sindrome di prune belly. Minerva Pediatr 27:1794PubMedGoogle Scholar
  33. 33.
    Deklerk DP, Scott WW (1978) Prostatic maldeveleopment in the prune belly syndrome: A defect in prostatic stromal-epithelial interaction. J Urol 120:341PubMedGoogle Scholar
  34. 34.
    Della Porta A, Mussa GC (1960) Atrofia parziale congenita dei muscoli abdominale (Illustrazione di un caso). Minerva Pediatr 12:1181Google Scholar
  35. 35.
    Dudgeon JA (1971) Cytomegalovirus infection. Arch Dis Child 46:581PubMedCrossRefGoogle Scholar
  36. 36.
    Eachempati U, Woods RE (1975) Cytomegalic virus disease in pregnancy. Obstet Gynecol 47:615Google Scholar
  37. 37.
    Eagle JF, Barrett GS (1950) Congenital deficiency of abdominal musculature with associated genitourinary abnormalities: A syndrome. Report of nine cases. Pediatrics 6:721PubMedGoogle Scholar
  38. 38.
    Ebert W (1967) Zur Frage der loaklisierten und generalisierten Cytomegalie und ihre Bedeutung für die Entstehung von Fehlbildungen. Z Kinderheilkd 98:350PubMedCrossRefGoogle Scholar
  39. 39.
    Ehrlich RM, Brown WJ (1977) Ultrastructural anatomic observations of the ureter in the prune belly syndrome. Birth Defects 13:101PubMedGoogle Scholar
  40. 40.
    Embil JA, Ozere RL, Haidane EV (1970) Congenital cytomegalovirus infection in two siblings from consecutive pregnancies. J Pediatr 77:417PubMedCrossRefGoogle Scholar
  41. 41.
    Enders-Ruckle G, Haas R, Luthardt T (1973) Virusinfektionen in der Schwangerschaft. Med Klin 68:1643PubMedGoogle Scholar
  42. 42.
    Engel RME (1974) C 27 — Prune belly syndrome in a female. Birth Defects 10:180Google Scholar
  43. 43.
    Flamm J, Kiesswetter H, Grof F (1980) Das Prune-Belly-Syndrom. Pädiatr Pädol 15:27PubMedGoogle Scholar
  44. 44.
    Frank DJ, de Vaux WD, Perkins JR, Perrin EV (1966) Fetal ascites and cytomegalic inclusion disease. Am J Dis Child 112:604PubMedGoogle Scholar
  45. 45.
    Gaboardi F, Sterpa A, Thibat E, Coruali R, Manfredini M, Bianchi C, Giacomondi MA, Bertagnoli L (1982) Prune belly syndrome: Report of three siblings. Helv Pediatr Acta 37:283Google Scholar
  46. 46.
    Garlinger P, Ott J (1974) Prune belly syndrome. Possible genetic implications. Birth Defects 10:173PubMedGoogle Scholar
  47. 47.
    Genoud J, Guibaud P, Bethenod M (1974) Cytomegalovirus and penta-X-syndrome. J Pediatr 85:869PubMedCrossRefGoogle Scholar
  48. 48.
    Goetz O (1972) Zytomegalie. Med Klin 67:1619PubMedGoogle Scholar
  49. 49.
    Gomirato-Sandrucci M, Vignolo-Lutati U (1957) Considerazioni sulla atrofia congenita della muscolatura addominale. Illustrazione di due casi. Minerva Pediatr 12:315Google Scholar
  50. 50.
    Graham CB, Thal A, Wassum CS (1970) Rubella-like bone changes in congenital cytomegalic inclusion disease. Radiology 94:39PubMedGoogle Scholar
  51. 51.
    Greinacher I, Straub E (1977) Das Prune-Belly-Syndrom und dessen inkomplette Formen. Monatsschr Kinderheilkd 125:325PubMedGoogle Scholar
  52. 52.
    Grenet P, Le Calve G, Badonel J, Gallet JP, Babinet JM (1972) Aplasie congénitale de la paroi abdominale. Ann Pédiatr (Paris) 19:523Google Scholar
  53. 53.
    Grossmann H, Winchester PH, Waldbaum RS (1970) Syndrome of congenital deficiency of abdominal wall musculature and associated genitourinary anomalies (prune belly syndrome). Progr Pediatr Radiol 3:327Google Scholar
  54. 54.
    Hagmann R, Kuffer F, Moser R, Bettex M (1969) Zytomegalie bei Megakolon. Schweiz Med Wochenschr 99:17PubMedGoogle Scholar
  55. 55.
    Halbrecht I, Komlos L, Shabtai F (1972) Prune belly syndrome with chromosomal fragment. Am J Dis Child 123:518PubMedGoogle Scholar
  56. 56.
    Hammond JA, van den Ende EW, Boardman RG, Mather BP (1974) Prune belly syndrome. South Afr Med J 48:839Google Scholar
  57. 57.
    Hannington-Kiff JG (1970) Prune belly syndrome and general anaesthesia. Br J Anaesth 42:649PubMedCrossRefGoogle Scholar
  58. 58.
    Hansen OM, Zachariae L (1959) Arthrogryposis multiplex congenita mit sekundärer Skoliose infolge von Bauchmuskelhypoplasie. Ann Paediatr 192:306PubMedGoogle Scholar
  59. 59.
    Hanshaw JB (1970) Developmental abnormalities associated with congenital cytomegalovirus infections. Adv Teratol 4:64Google Scholar
  60. 60.
    Hanshaw JB (1976) Cytomegalovirus. In: Remington JO, Klein WS (eds) Infectious diseases of the fetus and newborn infant. Saunders, Philadelphia London TorontoGoogle Scholar
  61. 61.
    Harley LM, Chen Y, Rattner WH (1972) Prune belly syndrome. J Urol 108:174PubMedGoogle Scholar
  62. 62.
    Hecker WC (1975) Anomalien im Bereich der Bauchwand. Bauchmuskeldefekte. In: Joppich G (Hrsg) Lehrbuch der Kinderheilkunde, 23. Aufl. Fischer, Stuttgart, S 288–289Google Scholar
  63. 63.
    Heffner RR (1970) Syndrome of absent abdominal muscles: Two cases with microcephaly, polymicrogyria and cerebellar malformations. J Neurol Neurosurg Psychiatry 33:844PubMedCrossRefGoogle Scholar
  64. 64.
    Helbig G (1962) Zum Krankheitsbild des angeborenen Bauchmuskeldefektes. Arch Kinderheilkd 165:68Google Scholar
  65. 65.
    Helbig P (1964) Mißbildungen der vorderen Bauchwand und ihre Behandlung. MMW 106:2047Google Scholar
  66. 66.
    Henley WL, Hyman A (1953) Absent abdominal musculature, genitourinary anomalies and deficiency in pelvic autonomic nervous system. Am J Dis Child 86:795Google Scholar
  67. 67.
    Heydenrych JJ, du Toit DF (1978) Torsion of the spleen and associated ‘prune belly syndrome’. A case report and review of the literature. South Afr Med J 53:637Google Scholar
  68. 68.
    Hildebrandt RJ, Sever JL, Margileth AM, Callagan DA (1967) Cytomegalovirus in the normal gregnant woman. Am J Obstet Gynecol 98:1125PubMedGoogle Scholar
  69. 69.
    Hultquist G, Nordvall S, Sundström C (1973) Insulitis in cytomegalovirus infection in a newborn infant. Ups J Med Sci 78:139PubMedCrossRefGoogle Scholar
  70. 70.
    Ives EJ (1974) The abdominal muscle deficiency triad syndrome — experience with ten cases. Birth Defects 10:127PubMedGoogle Scholar
  71. 71.
    Jäger J (1966) Kasuistische Mitteilungen und Schrifttumsübersicht zum kongenitalen Bauch-muskeldefektsyndrom. Pädiatr Grenzgeb 5:307PubMedGoogle Scholar
  72. 72.
    Jeffs RD, Comisarow RH, Hanna MK (1977) The early assessment for individualized treatment in the prune belly syndrome. Birth Defects 13:97PubMedGoogle Scholar
  73. 73.
    Käckell MY (1968) Okkulte connatale Cytomegalie. Ein Beitrag zur Diagnostik. Monatsschr Kinderheilkd 116:234PubMedGoogle Scholar
  74. 74.
    Kind C (1961) Generalisierte Cytomegalie bei einengen Zwillingen. Schweiz Med Wochenschr 1:15Google Scholar
  75. 75.
    King CR, Prescott G (1978) Pathogenesis of the prune-belly-anomalad. J Pediatr 93:273PubMedCrossRefGoogle Scholar
  76. 76.
    King RL, Tucker AS, Persky L (1961) Congenital hypoplasia of the abdominal muscles and associated genitourinary tract abnormalities. Radiology 77:228PubMedGoogle Scholar
  77. 77.
    Kirks DR, Taybi H (1975) Prune belly syndrome. An unusual cause of neonatal abdominal calcification. Am J Roentgenol Radium Ther Nucl Med 123:778PubMedGoogle Scholar
  78. 78.
    Korones SB, Todaro J, Roane JA, Sever JL (1970) Maternal virus infection after the first trimester of pregnancy and status of offspring to 4 years of age in a predominately Negro population. J Pediatr 77:245PubMedCrossRefGoogle Scholar
  79. 79.
    Krech U, Jung M (1968) Virologische Untersuchungen zur Abklärung intrauteriner Keimschäden. Ther Umsch 25:182PubMedGoogle Scholar
  80. 80.
    Krech U, Jung M, Jung F, Singeisen C (1968) Virologische und klinische Untersuchungen bei konnatalen und postnatalen Cytomegalien. Schweiz Med Wochenschr 38:1459Google Scholar
  81. 81.
    Krech U, Konjajew Z, Jung M (1971) Congenital cytomegalovirus infection in siblings from consecutive pregnancies. Helv Paediatr Acta 26:355PubMedGoogle Scholar
  82. 82.
    Kreil RL, Gates GA, Wulff H, Powell N, Poland JD, Chin TDY (1970) Cytomegalovirus isolations associated with pregnancy wastage. Am J Obstet Gynecol 106:885Google Scholar
  83. 83.
    Kroh G (1965) Beitrag zurm Krankheitsbild des angeborenen Bauchmuskeldefektes und der mit ihm verbundenen Anomalien im Bereich des Urogenital-und Darmtraktes. Urologe 4:191PubMedGoogle Scholar
  84. 84.
    Krugman S, Word R, Katz SL (1977) Cytomegalovirus infections. In: Infections diseases of children, 6th edn. Mosby, St. Louis, pp 1–12Google Scholar
  85. 85.
    Lang DJ (1966) The association of indirect inguinal hernia with congenital cytomegalic inclusion disease. Pediatrics 38:913PubMedGoogle Scholar
  86. 86.
    Lang DJ (1975) The epidemiology of cytomegalovirus infections: Interpretation of recent observations. In: Krugman S, Gershon AA (eds) Infections of the fetus and the newborn infant, 1st edn. Liss, New York, pp 35–45Google Scholar
  87. 87.
    Lang DJ, Noren B (1968) Cytomegaloviremia following congenital infection. J Pediatr 73:812PubMedCrossRefGoogle Scholar
  88. 88.
    Langman J (1974) Medizinische Embryologie, 3. Aufl. Thieme, StuttgartGoogle Scholar
  89. 89.
    Lattimer JK (1958) Congenital deficiency of the abdominal musculature and associated genitourinary anomalies: A report of 22 cases. J Urol 79:343PubMedGoogle Scholar
  90. 90.
    Lee SM (1977) Prune belly syndrome in a 54 year old man. JAMA 237:2216PubMedCrossRefGoogle Scholar
  91. 91.
    Leiber B (1976) Mißbildungsprobleme heute. Medizin 4:1511Google Scholar
  92. 92.
    Leiber B, Olbrich G (1972) Die klinischen Syndrome, 5. Aufl. Urban & Schwarzenberg, München Berlin Wien, S 81Google Scholar
  93. 93.
    Lester LA, Arcilla RA (1978) Chronic obstructive lung disease in infants with ventricular septal defects. J Pediatr 92:344PubMedCrossRefGoogle Scholar
  94. 94.
    Le-Tan-Vinh, Tran-Van-Duc, Thieffry S, Lelong M (1973) Association de malformation congénitale et de cytomégalie. Etude de 18 observations anatomo-cliniques. Nouv Presse Méd 2:1411PubMedGoogle Scholar
  95. 95.
    Lockhart JL, Reeve HR, Krueger RP, Glenn JF, Henry HH (1978) Megalourethra. Urology 12:333CrossRefGoogle Scholar
  96. 96.
    Lubinsky M, Rapoport P (1983) Transient fetal hydrops and “prune belly” in one identical female twin. N Engl J Med 308:256PubMedCrossRefGoogle Scholar
  97. 97.
    Luthardt T, Todt R (1970) Leistungsfähigkeit und sinnvolle Anwendung der modernen Cytomegaliediagnostik. Monatsschr Kinderheilkd 118:394PubMedGoogle Scholar
  98. 98.
    Luthardt T (1976) Cytomegalie. Enke, Stuttgart (Bücherei des Pädiaters, Heft 75)Google Scholar
  99. 99.
    Marc J, Comte B, Dilhuydy JM, Tavernier J (1973) Anomalies urinaires et agénésies des muscles de la paroi abdominale. Prune-belly-syndrome. J Radiol Electrol 54:379Google Scholar
  100. 100.
    Mareschal JL, Garance P, Marcinski A, Souvegrain J (1974) Malformations de l’appareil uri-naire dans les aplasies des muscles de la paroi abdominale. J Radiol Electrol 55:81Google Scholar
  101. 101.
    Massimo L, Gemme G (1960) Malformazioni dell’apparato urinario e anomalie délia musco-latura abdominale. Minerva Pediatr 12:1314PubMedGoogle Scholar
  102. 102.
    Mathieu BJ, Goldowsky S, Chaset N, Mathieu PL (1953) Congenital deficiency of the abdominal muscles (with associated multiple anomalies). J Pediatr 42:92PubMedCrossRefGoogle Scholar
  103. 103.
    Mauermeyer W (1955) Über kongenitale Mißbildungen an den Hornorganen, vergesellschaftet mit fehlender Bauchdeckenmuskulatur. Z Kinderheilkd 75:671CrossRefGoogle Scholar
  104. 104.
    McAllister RM, Wright HT, Tasem WM (1964) Cytomegalic inclusion disease in newborn twins. J Pediatr 64:278PubMedCrossRefGoogle Scholar
  105. 105.
    McCracken GH, Shinefield HR, Cobb K, Rausen AR, Dische MR, Eichenwald HF (1969) Congenital cytomegalic inclusion disease. Am J Dis Child 117:522PubMedGoogle Scholar
  106. 106.
    McElfresh AE, Arey JB (1957) Generalized cytomegalic inclusion disease. J Pediatr 51:146PubMedCrossRefGoogle Scholar
  107. 107.
    McEnery G, Stern H (1970) Cytomegalovirus infection in early infancy. Five atypical cases. Arch Dis Child 45:669PubMedCrossRefGoogle Scholar
  108. 108.
    McGovern JH, Marshall VF (1959) Congenital deficiency of the abdominal musculature and obstructive uropathy. Surg Gynecol Obstet 108:289PubMedGoogle Scholar
  109. 109.
    Medearis DN (1957) Cytomegalic inclusion disease. Analysis of clinical features based on the literature and six additional cases. Pediatrics 19:467PubMedGoogle Scholar
  110. 110.
    Medearis DN (1964) Observations concerning human cytomegalovirus infection and disease. Bull John Hopkins Hosp 114:181PubMedGoogle Scholar
  111. 111.
    Metrick S, Brown RH, Rosenblum A (1957) Congenital absence of the abdominal musculature and associated anomalies. Review of recent literature and four new cases. Pediatrics 19:1043PubMedGoogle Scholar
  112. 112.
    Mickel RE (1971) The “prune-belly” syndrome. South Afr J Surg (:45Google Scholar
  113. 113.
    Mildenberger H (1969) Das Bauchdeckenaplasie-Syndrom. Med Welt 23:1332PubMedGoogle Scholar
  114. 114.
    Mininberg DT, Montoya F, Okada K, Galioto F, Presutti R (1973) Subcellular muscle studies in the prune belly syndrome. J Urol 109:524PubMedGoogle Scholar
  115. 115.
    Monie IW, Monie BJ (1979) Prune belly syndrome and fetal ascites. Teratology 19:111PubMedCrossRefGoogle Scholar
  116. 116.
    Morales JC, Yamaguchi R (1970) Sindrome de prune belly. Minerva Pediatr 22:1338Google Scholar
  117. 117.
    Moser R, Graepel P, Bürki K, Kuffer F (1972) Intestinale Cytemegalie im Kindesalter: Elektronenmikroskopische Untersuchung an in vivo gewonnenem Material. Zentralbl allg Pathol 195:385Google Scholar
  118. 118.
    Navin JJ, Angevine JM (1968) Congenital cytomegalic inclusion disease with porencephaly. Neurology 18:470PubMedGoogle Scholar
  119. 119.
    Niggemeyer H, Sandhage K (1972) Marginalien zur Thymushyperplasie: Angeboren in Kombination mit Nebennierenryperplasie und Zytomegalie bzw. Myokarditis. Klin Pädiatr 184:501Google Scholar
  120. 120.
    North AF, Eldredge DM, Talpey WB (1966) Abdominal distention at birth. Due to ascites associated with obstructive uropathy. Am J Dis Child 111:613PubMedGoogle Scholar
  121. 121.
    Nunn IN, Stephens FD (1961) The triad syndrome: A composite anomaly of the abdominal wall, urinary system and testes. J Urol 86:782PubMedGoogle Scholar
  122. 122.
    Obrinsky W (1949) Agenesis of abdominal muscles with associated malformation of the genitourinary tract: A clinical syndrome. Am J Dis Child 77:362PubMedGoogle Scholar
  123. 123.
    Oehme J (1973) Klinik der Cytomegalie. Klin Wochenschr 51:523PubMedCrossRefGoogle Scholar
  124. 124.
    O’Kell RT (1969) Embryonic abdominal musculature associated with anomalies of the genitourinary and gastrointestinal systems. Am J Obstet Gynecol 105:1283PubMedGoogle Scholar
  125. 125.
    Okulski TA (1978) The prenatal diagnosis of lower urinary tract obstruction using B scan ultrasound: A case report. J din Ultrasound 5:268CrossRefGoogle Scholar
  126. 126.
    Oppenheimer EH, Esterly JF (1973) Cytomegalovirus infection: A possible cause of biliary atresia. Am J Pathol 71:2aGoogle Scholar
  127. 127.
    Overall JC, Glasgow LA (1970) Virus infections of the fetux and newborn infant. J Pediatr 77:315PubMedCrossRefGoogle Scholar
  128. 128.
    Pagon RA, Smith DW, Shepard TH (1979) Urethral obstruction malformation complex: A cause of abdominal muscle deficiency and the “prune belly”. J Pediatr 94:900PubMedCrossRefGoogle Scholar
  129. 129.
    Pal SR, Das KC, Chitkara NL, Bhakoo ON (1972) Cytomegalovirus infection of two neonates with evidence of lympho-proliferation. Indian J Med Res 60:815PubMedGoogle Scholar
  130. 130.
    Palmer JM, Tesluk H (1974) Urethral pathology in the prune belly syndrome. J Urol 111:701PubMedGoogle Scholar
  131. 131.
    Palmtag H, Dreikorn K, Röhl L (1979) Urodynamic studies in prune belly syndrome. A case report. Scand J Urol Nephrol 13:11PubMedCrossRefGoogle Scholar
  132. 132.
    Pansadoro V, Marzetti GF, Fasanelli S, Pulone M (1974) Trattamento delle malformazioni urinarie in un caso die “prune belly syndrome”. Minerva Pediatr 26:1606PubMedGoogle Scholar
  133. 133.
    Perlmutter AD (1976) Reduction cystoplasty in prune belly syndrome. J Urol 116:356PubMedGoogle Scholar
  134. 134.
    Petersen DS, Fish L, Cass AS (1972) Twins with congenital deficiency of abdominal musculature. J Urol 107:670PubMedGoogle Scholar
  135. 135.
    Pichler E, Schön R (1972) Extrahepatische Gallengangsatresie und Cytomegalie, kausaler Zusammenhang oder Koinzidenz? Z Kinderheilkd 112:261CrossRefGoogle Scholar
  136. 136.
    Plotkin SA, Pasquriello PS (1969) Congenital cytomegalovirus infection associated with multicystic kidney. Am J Dis child 118:515PubMedGoogle Scholar
  137. 137.
    Pomponio N, Argento MP (1960) Su due casi di sindrome malformativa multipla di Obrinsky. Minerva Pediatr 12:1481PubMedGoogle Scholar
  138. 138.
    Pramanik AK, Altshuler G, Light IJ, Sutherland JM (1977) Prune-belly-syndrome associated with Potter (renal nonfunction) syndrome. Am J Dis Child 131:672PubMedGoogle Scholar
  139. 139.
    Qazi QH, Kuaffman S, Sher J, Mapa HC (1973) Chromosomal abnormality in prune belly syndrome. Humangenetik 20:265PubMedCrossRefGoogle Scholar
  140. 140.
    Quan A, Strauss L (1962) Congenital cytomegalic inclusion disease. Am J Obstet Gynecol 83:1240PubMedGoogle Scholar
  141. 141.
    Rabinowitz R, Schillinger JF (1977) Prune belly syndrome in the female subject. J Urol 118:454PubMedGoogle Scholar
  142. 142.
    Rabinowitz R, Barkin TK, Schillinger JF, Jeffs RD (1978) Urinary tract reconstruction in prune belly syndrome. Urology 12:333PubMedCrossRefGoogle Scholar
  143. 143.
    Randolph JG (1977) Total surgeical reconstruction for patients with abdominal muscular deficiency (“prune belly”) syndrome. J Pediatr Surg 12:1033PubMedCrossRefGoogle Scholar
  144. 144.
    Reybaud C, Martinon J, Clement M, Pierron H, Orsini A (1967) Aplasie congénitale de la paroi abdominale avec amlformations viscérales multiples. Pédiatrie 22:737Google Scholar
  145. 145.
    Reynolds DW, Stagno S, Stubbs KG, Dahle AJ, Livingston MM, Saxon SS, Alford CA (1974) Inapparent congenital cytomegalovirus infection with elevated cord IgM levels. Causal relation with auditory and mental deficiency. New Engl J Med 290:291PubMedCrossRefGoogle Scholar
  146. 146.
    Rezza E, Midulla M, Zardi O, Marzetti G, Castello M, Pana A (1971) Cytomegalovirus infection in childhood: Clinical pictures and long term evaluation. In: XIII. Internationaler Kongress für Pädiatrie, Wien. Verlag der Wiener Medizinischen Akagemie, Wien (Kongressberichte, Bd VI, S 315)Google Scholar
  147. 147.
    Riccardi VM, Grum CM (1977) The prune belly anomaly. Heterogeneity and superficial x-linkage mimicry. J Med Genet 14:266PubMedCrossRefGoogle Scholar
  148. 148.
    Ricci S, Jasonni V (1974) La sindrome de deficienza della muscolatura addominale (c.d. AMD o prune-belly-syndrome). Minerva Pediatr 26:1627PubMedGoogle Scholar
  149. 149.
    Rogers LW, Ostrow PT (1973) The prune belly syndrome. Report of 20 cases and description of a lethal variant. J Pediatr 83:786PubMedCrossRefGoogle Scholar
  150. 150.
    Romanet P, Aira G, Payet G (1980) Aplasie congénitale de la musculature de la paroi abdominale “Prune belly syndrome”. Arch Fr Pédiatr 37:401PubMedGoogle Scholar
  151. 151.
    Ruprecht KW, Treske U (1970) Das Bauchdeckenaplasie-Syndrom (Obrinsky). Eine urogenitale Systemmißbildung. Dtsch Med Wochenschr 95:327PubMedCrossRefGoogle Scholar
  152. 152.
    Salmon MA, Lindenbaum RH (1978) Developmental defects and syndromes, 1st edn. HM+M Publishers, Aylesburg, p 286Google Scholar
  153. 153.
    Sellers BB, McNeal R, Smith RV, Griswold WR, Mendoza SA (1976) Congenital megalourethara associated with prune belly syndrome. J Urol 116:814PubMedGoogle Scholar
  154. 154.
    Shenasky JH, Whelchel JD (1976) Renal transplantation in prune belly syndrome. J Urol 115:112PubMedGoogle Scholar
  155. 155.
    Silverman FN, Huang N (1950) Congenital absence of the abdominal muscles. Associated with malformation of the genitourinary and alimentary tracts. Report of cases and review of literature. Am J Dis Child 80:91PubMedGoogle Scholar
  156. 156.
    Sladczyk E (1967) Das gehäufte familiäre Auftreten des angeborenen Bauchmuskelwanddefektes. Zentralbl Chir 11:426Google Scholar
  157. 157.
    Smith DW (1979) Redundant skin folds in the infant — their origin and relevance. J Pediatr 94:1021PubMedCrossRefGoogle Scholar
  158. 158.
    Smithells RW (1978) Drugs, infections and congenital abnormalities. Arch Dis Child 53:93PubMedCrossRefGoogle Scholar
  159. 159.
    Snyder HM, Harrison NW, Whitfield HN, Williams DI (1976) Urodynamics in the prune belly syndrome. Br J Urol 48:663PubMedCrossRefGoogle Scholar
  160. 160.
    Spence HM, Allen T (1964) Congenital absence of abdominal musculature. Urologic aspects. JAMA 187:126Google Scholar
  161. 161.
    Stagno S, Reynolds DW, Labeman A, Charamella LJ, Alford CA (1973) Congenital cytomegalovirus infection: Consecutive occurrence due to viruses with similar antigenic composittions. Pediatrics 52:788PubMedGoogle Scholar
  162. 162.
    Stanga E (1956) Über multiple Abartungen mit Flughautbildung (Pterygium-Syndrom) und kongenitale Aplasie der Bauchdeckenmuskulatur. Ann Padiatr (Paris) 187:384Google Scholar
  163. 163.
    Starr JG, Bart RD, Gold E (1970) Inapparent congenital cytomegalovirus infection. Clinical and epidemiologic characteristics in early infancy. New Engl J Med 282:1075PubMedCrossRefGoogle Scholar
  164. 164.
    Stern H (1968) Isolation of cytomegalovirus and clinical manifestations of infection at different ages. Br Med J 1:665PubMedCrossRefGoogle Scholar
  165. 165.
    Stern H, Tucker SM (1965) Cytomegalovirus infection in the newborn and in early childhood. Three atypical cases. Lancet 2:1268Google Scholar
  166. 166.
    Stöber U, Strohmeyer P (1979) Überlegungen zum operativen Vorgehen beim Prune-Belly-Syndrom. Symptomatik — Diagnostik — Harnableitung. Z Kinderheilkd 26:132Google Scholar
  167. 167.
    Straub E, Spranger J (1980) Prune belly syndrome and urethral obstruction. J Pediatr 96:776PubMedCrossRefGoogle Scholar
  168. 168.
    Sturbois G, Mingeot R, Lamy ME (1974) Infection virale et grossesse. Expérience personnelle et données de la litterature. J Gynecol Obstet Biol Reprod (Paris) 3:201Google Scholar
  169. 169.
    Symonds DA, Driscoll SG (1974) Massive fetal ascites, urethral atresia and cytomegalic inclusion disease. Am J Dis Child 127:895PubMedGoogle Scholar
  170. 170.
    Thomas IT, Smith DW (1974) Oligohydramnios, cause of the nonrenal features of Potter’s syndrome, including pulmonary hypoplasia. J Pediatr 84:811PubMedCrossRefGoogle Scholar
  171. 171.
    Tuch BA, Smith TK (1978) Prune belly syndrome. A report of twelve cases and review of the literature. J Bone Joint Surg (Am) 60:109Google Scholar
  172. 172.
    Uehling DT, Baumüller A, Chesney R (1977) Urologische Probleme beim Bauchdeckenaplasiesyndrom. Urologe (Ausg A) 16:283Google Scholar
  173. 173.
    Vargas AD (1977) Pyeloileovesical diversion in a case of prune belly syndrome. J Urol 118:886PubMedGoogle Scholar
  174. 174.
    Vullièmoz P, Lurie D, Obolensky W (1969) La cytomégalie. Gynaecologia 168:484PubMedGoogle Scholar
  175. 175.
    Waldbaum RS, Marshall VF (1970) The prune belly syndrome: A diagnostic therapeutic plan. J Urol 103:668PubMedGoogle Scholar
  176. 176.
    Wayne ER, Burrington JP, Myers DN, Cotton E, Block W (1973) Bilateral eventration of the diaphragm in a neonate with congenital cytomegalic inclusion disease. J Pediatr 83:164PubMedCrossRefGoogle Scholar
  177. 177.
    Weber ML, Rivard G, Perreault G (1978) Prune belly syndrome associated with congenital cystic adenomatoid malformation of the lung. Am J Dis Child 132:316PubMedGoogle Scholar
  178. 178.
    Welch KJ, Kearney GP (1974) Abdominal musculature deficiency syndrome: Prune belly. J Urol 111:693PubMedGoogle Scholar
  179. 179.
    Welling P, Pfeiffer RA, Kosenow W, Bliesener JA, Jones KV, Haarmeyer A (1975) Beobachtungen zum Bauchmuskelaplasie-Syndrom. Z Kinderheilkd 118:315PubMedCrossRefGoogle Scholar
  180. 180.
    Widersberg H, Lambrecht R (1983) Beitrag zur Morphologie des Bauchmuskelaplasiesyndroms. Zentralbl Allg Pathol 127:181Google Scholar
  181. 181.
    Wigger HJ, Blanc WA (1977) The prune belly syndrome. Pathol Annu 12:17PubMedGoogle Scholar
  182. 182.
    Willert C, Cohen A, Yu YT, Madden JD (1978) Association of prune belly syndrome and gastroschisis. Am J Dis Child 132:526PubMedGoogle Scholar
  183. 183.
    Williams DI, Burkholder GV (1967) The prune belly syndrome. J Urol 98:244PubMedGoogle Scholar
  184. 184.
    Wilson SK, Moore GW, Hutchins GM (1978) Congenital cystic adenomatoid malformation of the lung associated with abdominal musculature deficiency (Prune belly). Pediatrics 62:421PubMedGoogle Scholar
  185. 185.
    Wiltschke H (1969) Urologische Probleme bei der kongenitalen Bauchmuskelaplasie. Wien Klin Wochenschr 81:776Google Scholar
  186. 186.
    Woodard JR (1978) The prune belly syndrome. Urol Clin North Am 5:75PubMedGoogle Scholar
  187. 187.
    Woodard JR, Parrot TS (1978) Reconstruction of the urinary tract in prune belly uropathy. J Urol 119:824PubMedGoogle Scholar
  188. 188.
    Woodhouse CRJ, Wansley PG, Innes-Williams DC (1982) Prune belly syndrome — report of 47 cases. Arch Dis Child 57:856PubMedCrossRefGoogle Scholar
  189. 189.
    Wright HT (1971) Cytomegalic inclusion disease of infancy: An expanded syndrome. In: XIII. Internationaler Kongress für Pädiatrie, Wien. Verlag der Wiener Medizinischen Akademie, Wien (Kongtessberichte, Bd VI)Google Scholar
  190. 190.
    Wright HT, Parker CE, Mavalwala J (1972) Unusual dermoglyphic findings associated with cytomegalic inclusion disease of infancy. A first report and practical review. Calif Med 116:14PubMedGoogle Scholar

Copyright information

© Springer-Verlag Berlin Heidelberg 1984

Authors and Affiliations

  • B. H. Belohradsky
    • 1
  • C. Henkel
    • 2
  1. 1.Kinderklinik der Universtität im Dr. von Haunerschen KinderspitalMünchen 2Deutschland
  2. 2.Gynäkologischgeburtshilfliche AbteilungStädtisches Krankenhaus München-HarlachingMünchen 90Deutschland

Personalised recommendations