Abstract
When, 44 years ago, Fanconi et al. (228) published their paper on “Das Coeliakie-Syndrom bei angeborener cystischer Pankreasfibromatose und Bronchiektasien”, they were of the opinion that they were reporting on a very rare syndrome that in most cases led to death at an early age. In 1957 Bachmann (31), in Vol. 8 of this series, summarized the available knowledge on “the so-called cystic fibrosis of the pancreas”; he expressed the hope that an improvement in our knowledge of the etiology of the disease could lead to an improvement in the results of its treatment.
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References
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Stephan, U., Götz, M., Stephan, K., Bender, S. (1980). Cystic Fibrosis. In: Frick, P., von Harnack, GA., Martini, G.A., Prader, A., Wolff, H.P. (eds) Ergebnisse der Inneren Medizin und Kinderheilkunde / Advances in Internal Medicine and Pediatrics. Ergebnisse der Inneren Medizin und Kinderheilkunde. Neue Folge Advances in Internal Medicine and Pediatrics, vol 44. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-67557-7_3
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