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Neurometabolische Krankheiten

  • Biörn Ivemark

Zusammenfassung

Neurometabolische Krankheiten bedeuten Schädigungen des Zentralnervensystems bei abnormem Stoffwechsel. Zum Teil spielt sich bei diesen Krankheiten der pathologische Prozeß einzig oder hauptsächlich im Nervensystem ab. Beim Großteil der hierhergehörenden Krankheiten ist der Befall des Nervensystems jedoch nur eine Teilmanifestation einer generalisierten metabolischen Störung. Dieses Kapitel soll auf jene Krankheiten beschränkt bleiben, die lichtmikroskopischer Diagnostik, hauptsächlich an Biopsiematerial, zugänglich sind. Die mikroskopische Untersuchung bei metabolischen Leiden ist indessen selten diagnostisch genügend. Die morphologischen Veränderungen müssen so oft wie möglich mit biochemischen Befunden verglichen werden.

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Literatur

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Refsumsche Krankheit

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Sulfatidose

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Wilsonsche Krankheit

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Zahnextraktion

  1. Anneroth, G., Ivemark, B. I.: Histochemical localization of lipids in human dental pulp. Svensk Tandläk.-T. 63, 747 (1970).Google Scholar
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Copyright information

© Biörn Ivemark und Almqvist & Wiksell Förlag AB, Stockholm 1971

Authors and Affiliations

  • Biörn Ivemark
    • 1
  1. 1.Institutet för pediatrisk patologiKarolinska sjukhusetStrockholm 60Schweden

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