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Prionkrankheiten (transmissible spongiforme Enzephalopathien)

  • H. A. Kretzschmar

Zusammenfassung

Prionkrankheiten sind übertragbare neurodegenerative Krankheiten, die bei Mensch und Tier auftreten (Prusiner 1998) (Tabellen 11.1–11.3). Klinisch gehen sie mit einer meist stark ausgeprägten Demenz und verschiedenen neurologischen Veränderungen wie Ataxie, Myoklonien oder Erblindung einher; sie nehmen immer einen tödlichen Verlauf.

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  • H. A. Kretzschmar

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