Zusammenfassung
Eine gestörte Repolarisation mit verlängerter QT-Zeit im Oberflächen-EKG und verlängertem Aktionspotential auf zellulärer Ebene gilt als Ursache potentiell lebensbedrohlicher ventrikulärer Arrhythmien. Das angeborene Long-QT-Syndrom wurde in diesem Zusammenhang lange als Rarität angesehen und dient heute als molekulares Modell zum Verständnis der ventrikulären Arrhythmogenese.
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Kääb, S. (1999). Long-QT-Syndrom: molekulare Grundlagen und Klinik. In: Hoffmann, E., Steinbeck, G. (eds) Interventionelle kardiale Elektrophysiologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-58522-7_4
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DOI: https://doi.org/10.1007/978-3-642-58522-7_4
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