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Erbliche Hauterkrankungen

  • Wolfgang Küster
Part of the Handbuch der Molekularen Medizin book series (HDBMOLEK, volume 7)

Zusammenfassung

Unter erblichen Hauterkrankungen (Genodermatosen) werden Erkrankungen der Haut und ihrer Anhangsgebilde verstanden, die durch die Verßnderung einer einzigen Erbanlage bedingt sind, also monogen entsprechend den Mendel-Regeln vererbt werden. Zu den Genodermatosen lassen sich als wichtigste Erkrankungsgruppen benennen: Verhornungsstörungen, blasenbildende Erkrankungen, Bindegewebsstörungen, Aplasien und Anomalien, Störungen des Ektoderms, Pigmentanomalien, Haar- und Nagelerkrankungen, Erkrankungen der Mundschleimhaut sowie der Blut- und Lymphgefßße, Störungen der Talg- und Schweißdrüsen, Stoffwechsel- und Immundefekte, benigne und maligne Tumoren.

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© Springer-Verlag Berlin Heidelberg 2000

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  • Wolfgang Küster

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