• Brigitte Royer-Pokora
  • Valérie Schumacher
Part of the Molekulare Medizin book series (MOLMED)


Wilms-Tumoren sind hochmaligne embryonale Mischgeschwulste der Nieren und gehören mit 7% zu den häufigsten soliden Tumoren des Kindesalters, die meist vor dem 5. Lebensjahr diagnostiziert werden. Sporadischer Wilms-Tumor tritt bei 1/10000 Lebendgeburten auf und ist meist unilateral. Ungefähr 1–2% der Patienten mit Wilms-Tumor haben betroffene Verwandte, dabei sind Geschwister und Kusinen am häufigsten betroffen.


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Copyright information

© Springer-Verlag Berlin Heidelberg 2001

Authors and Affiliations

  • Brigitte Royer-Pokora
    • 1
  • Valérie Schumacher
    • 1
  1. 1.Heinrich-Heine-Universität Medizinische EinrichtungenInstitut für Humangenetik und AnthropologieDüsseldorf

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