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Hämochromatose (hereditäre Hämochromatose, sekundäre Eisenüberladungssyndrome)

  • J. Kaltwasser
  • W. F. Caspary

Zusammenfassung

Die hereditäre (genetische) Hämochromatose ist eine genetisch bedingte Krankheit, bei der Mutationen des HFE-Gens eine erhöhte intestinale Eisenresorption bewirken. Die klinischen Manifestationen sind durch Eisenablagerungen in Geweben wie Leber, Pankreas und Herz bedingt. Wenn die Diagnose früh gestellt und eine Aderlass-Therapie frühzeitig eingeleitet wird, haben die Patienten eine normale Lebenserwartung.

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Copyright information

© Springer-Verlag Berlin Heidelberg 2001

Authors and Affiliations

  • J. Kaltwasser
  • W. F. Caspary

There are no affiliations available

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