Zusammenfassung
Unter Porphyrien versteht man Stoffwechselkrankheiten, die durch eine Störung der Hämbiosynthese gekennzeichnet sind. Die traditionelle Einteilung dieser Erkrankungen in hepatisehe und erythropoetische Formen ist unscharf, da es Überschneidungen gibt. Auch bei den erythropoetischen Porphyrien kann die Leber mehr oder weniger betroffen sein.
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Sahm, S.W., Caspary, W.F. (2001). Porphyrien. In: Caspary, W.F., Leuschner, U., Zeuzem, S. (eds) Therapie von Leber- und Gallekrankheiten. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-56819-0_11
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DOI: https://doi.org/10.1007/978-3-642-56819-0_11
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