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Radiotherapy of Intraocular and Orbital Tumors pp 129–136Cite as

Orbital Rhabdomyosarcoma

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Part of the book series: Medical Radiology ((Med Radiol Radiat Oncol))

Abstract

Rhabdomyosarcoma (RMS) accounts for 4–8% of malignancies in children under 15 years old (CRIST et al. 1990). RMS is the most common orbital malignancy in children and was the primary site in 65 of 686 (9.47%) patients reported in the Intergroup RMS studies I and II (Crist et al. 1990). Knowles et al. (1978) gathered data from four major reviews (Ashton and Morgan 1965; Frayer and Enterline 1959; Jones et al. 1965; Porterfield and Zimmerman 1962); of 161 patients, 64 (40%) were 0–5 years old, 57 (35%) were 6–10 years, 28 (17%) were 11–15 years, 7 (4%) were 16–20 years, 3 (2%) were 21–25 years, and 2 (1%) were older than 25. The average age was approximately 8 years in each of the four reviews, and the median age was 6 years in the Intergroup RMS study. RMS is rare in the newborn and not common before 1 year. The oldest patient reported was 78 years of age (Kassel et al. 1965). Its occurrence during pregnancy has been reported (Olurin 1969).

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Author information

Authors and Affiliations

  1. Department of Radiation Oncology, SUNY Upstate Medical University, 750 E. Adams Street, Syracuse, NY, 13210, USA

    R. H. Sagerman MD, FACR

Authors
  1. R. H. Sagerman MD, FACR
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Editor information

Editors and Affiliations

  1. Department of Radiation Oncology, State University of New York Upstate Medical University, 750 East Adams Street, Syracuse, NY, 13210, USA

    Robert H. Sagerman MD, FACR (Professor) (Professor)

  2. Department of Radiotherapy and Radiooncology, University Hospital Hamburg-Eppendorf, Martinistrasse 52, 20246, Hamburg, Germany

    Winfried E. Alberti MD (Professor) (Professor)

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© 2003 Springer-Verlag Berlin Heidelberg

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Sagerman, R.H. (2003). Orbital Rhabdomyosarcoma. In: Sagerman, R.H., Alberti, W.E. (eds) Radiotherapy of Intraocular and Orbital Tumors. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-55910-5_13

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  • DOI: https://doi.org/10.1007/978-3-642-55910-5_13

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-63147-4

  • Online ISBN: 978-3-642-55910-5

  • eBook Packages: Springer Book Archive

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