Abstract
Many types of extrapancreatic lesions associated with immunoglobulin G (IgG)4-related autoimmune pancreatitis (type 1 AIP) are known. IgG4-related sclerosing cholangitis, retroperitoneal fibrosis, and sclerosing sialadenitis are particularly well known. Pulmonary involvement is not rare, but the mechanism is still difficult to fully understand. Pulmonary lesions associated with AIP were described in 2 separate case reports in 2004 [1, 2] and in our case series of 4 patients in 2006 [3]. Most were reported as interstitial pneumonia. However, it gradually became evident that there were various patterns in the pulmonary lesions [4–8]. Moreover, IgG4-related lesions were found in the mediastinum and pleura [5, 7–11]. It is possible that some types of airway disease, including bronchial asthma, belong to IgG4-related disease (IgG4) [12, 13]. Because there have been no diagnostic criteria, there appears to be no consensus on the definition of “pulmonary lesions” among specialists. In this article, intrathoracic lesions, in addition to lung parenchymal lesions, are discussed.
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Hirano, K. (2015). Pulmonary Lesions. In: Kamisawa, T., Chung, J. (eds) Autoimmune Pancreatitis. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-55086-7_19
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DOI: https://doi.org/10.1007/978-3-642-55086-7_19
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