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Cutaneous Lymphomas

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Clinical Atlas of Skin Tumors

Abstract

The skin may be affected by lymphoproliferative diseases either primarily or secondarily. In addition to skin involvement of systemic lymphomas, including Hodgkin disease and non-Hodgkin lymphomas, a heterogeneous group of primary cutaneous lymphomas (extranodal non-Hodgkin lymphomas) originating from B cells, T cells and NK (natural killer) cells, have been described. By definition, these lymphomas are restricted to the skin at the time of diagnosis but may show involvement of lymph nodes, visceral organs, and bone marrow during their course. However, some types of cutaneous lymphomas very rarely involve extracutaneous sites. In the last two decades, many classification systems of these diseases have been proposed. This chapter is mainly organized according to the WHO-EORTC (World Health Organization-European Organization for Research and Treatment of Cancer) classification of cutaneous lymphomas published in 2005 and the WHO classification of lymphomas published in 2008. Most of these primary cutaneous lymphomas included in these classification systems showing different clinical, histopathologic, cytogenetic, and molecular genetic features and prognosis will be discussed. Pseudolymphomas which are clinical and histopathologic imitators of lymphomas, and cutaneous infiltration of hematologic neoplasms are included in this chapter for convenience.

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Baykal, C., Yazganoğlu, K.D. (2014). Cutaneous Lymphomas. In: Clinical Atlas of Skin Tumors. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-40938-7_14

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  • DOI: https://doi.org/10.1007/978-3-642-40938-7_14

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-40937-0

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